Diffuse-Type Caroli Disease with Characteristic Central Dot Sign Complicated by Multiple Intrahepatic and Common Bile Duct Stones
Clinical Endoscopy
; : 400-403, 2017.
Article
em En
| WPRIM
| ID: wpr-195022
Biblioteca responsável:
WPRO
ABSTRACT
Caroli disease (CD) is a rare congenital malformation of the liver characterized by non-obstructive, segmental, cystic dilatation of the intrahepatic bile ducts (IHDs). The clinical course is usually asymptomatic for the first 5–20 years, and symptoms may seldom occur throughout the patient’s life. Bile stagnation leads to recurrent episodes of cholangitis, stone formation, or liver abscesses, and biliary cirrhosis usually occurs years later. Here we report on a 42-year-old man diagnosed with diffuse-type CD with a characteristic central dot sign, who had multiple intrahepatic and common bile duct (CBD) stones. CBD stones were treated successfully with endoscopic retrograde cholangiopancreatography (ERCP).
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Texto completo:
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Base de dados:
WPRIM
Assunto principal:
Bile
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Ductos Biliares Intra-Hepáticos
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Colangite
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Colangiopancreatografia Retrógrada Endoscópica
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Doença de Caroli
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Ducto Colédoco
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Coledocolitíase
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Dilatação
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Fígado
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Abscesso Hepático
Limite:
Adult
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Humans
Idioma:
En
Ano de publicação:
2017
Tipo de documento:
Article