The Management of Cardiovascular Abnormalities in Patient With LEOPARD Syndrome
Korean Circulation Journal
; : 339-342, 2010.
Article
em En
| WPRIM
| ID: wpr-196627
Biblioteca responsável:
WPRO
ABSTRACT
LEOPARD syndrome (LS) is a rare hereditary disorder in Asian countries. This syndrome consists of multiple systemic abnormalities. In particular, characteristic cardiovascular effects in LS may include variable clinical manifestations from benign to life-threatening courses. The cardiac effects of this syndrome consist of left ventricular hypertrophy (LVH), pulmonary stenosis (PS), coronary artery dilatation and electrocardiogram(ECG) abnormalities. Since there are few LS patients who have undergone a complete cardiovascular evaluation, the nature and clinical prognosis of cardiovascular abnormalities in this syndrome remain uncertain. Also, there have been few reports on therapeutic strategies for cardiovascular abnormalities in LS. Here we describe a case of LS who presented with multiple cardiovascular problems and underwent successful surgical and medical treatment.
Palavras-chave
Texto completo:
1
Base de dados:
WPRIM
Assunto principal:
Prognóstico
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Estenose da Valva Pulmonar
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Hipertrofia Ventricular Esquerda
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Anormalidades Cardiovasculares
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Vasos Coronários
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Síndrome LEOPARD
/
Povo Asiático
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Panthera
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Dilatação
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Lentigo
Tipo de estudo:
Prognostic_studies
Limite:
Humans
Idioma:
En
Ano de publicação:
2010
Tipo de documento:
Article