Chylous Manifestations and Management of Gorham-Stout Syndrome
The Korean Journal of Thoracic and Cardiovascular Surgery
; : 44-46, 2019.
Article
em En
| WPRIM
| ID: wpr-939203
Biblioteca responsável:
WPRO
ABSTRACT
Gorham-Stout disease (GSD) was first described by Gorham and colleagues in 1954, but its precise mechanism and cause remain to be elucidated. In this condition, voluminous and potentially fatal chylous effusions into the thorax can occur. Herein, we describe a case of GSD in which the patient presented with massive pleural effusions and mottled osteolytic bone lesions. We performed multiple operations, including thoracic duct ligation using video-assisted thoracoscopic surgery and thoracotomic decortication, but these procedures did not succeed in preventing recurrent pleural effusion and chest wall lymphedema. After administering sirolimus (0.8 mg/m2, twice a day) and propranolol (40 mg, twice a day), the process of GSD in this patient has been controlled for more than 2 years.
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Base de dados:
WPRIM
Idioma:
En
Ano de publicação:
2019
Tipo de documento:
Article