Detalhe da pesquisa
1.
Effect of VX-770 in persons with cystic fibrosis and the G551D-CFTR mutation.
N Engl J Med
; 363(21): 1991-2003, 2010 Nov 18.
Artigo
em Inglês
| MEDLINE | ID: mdl-21083385
2.
Results of a phase IIa study of VX-809, an investigational CFTR corrector compound, in subjects with cystic fibrosis homozygous for the F508del-CFTR mutation.
Thorax
; 67(1): 12-8, 2012 Jan.
Artigo
em Inglês
| MEDLINE | ID: mdl-21825083
3.
A pipeline of therapies for cystic fibrosis.
Semin Respir Crit Care Med
; 30(5): 611-26, 2009 Oct.
Artigo
em Inglês
| MEDLINE | ID: mdl-19760548
4.
Cystic fibrosis foundation: achieving the mission.
Respir Care
; 54(6): 788-95; discussion 795, 2009 Jun.
Artigo
em Inglês
| MEDLINE | ID: mdl-19467165
5.
Guidelines for diagnosis of cystic fibrosis in newborns through older adults: Cystic Fibrosis Foundation consensus report.
J Pediatr
; 153(2): S4-S14, 2008 Aug.
Artigo
em Inglês
| MEDLINE | ID: mdl-18639722
6.
Cancer risk in nontransplanted and transplanted cystic fibrosis patients: a 10-year study.
J Natl Cancer Inst
; 95(5): 381-7, 2003 Mar 05.
Artigo
em Inglês
| MEDLINE | ID: mdl-12618503
7.
Improving the care of infants identified through Cystic Fibrosis newborn screening.
J Pediatr
; 155(6 Suppl): S71-2, 2009 Dec.
Artigo
em Inglês
| MEDLINE | ID: mdl-19914444
8.
Azithromycin in patients with cystic fibrosis chronically infected with Pseudomonas aeruginosa: a randomized controlled trial.
JAMA
; 290(13): 1749-56, 2003 Oct 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-14519709
9.
Sweat chloride as a biomarker of CFTR activity: proof of concept and ivacaftor clinical trial data.
J Cyst Fibros
; 13(2): 139-47, 2014 Mar.
Artigo
em Inglês
| MEDLINE | ID: mdl-24660233
10.
Infections in cystic fibrosis.
Semin Pediatr Infect Dis
; 6(3): 174-181, 1995 Jul.
Artigo
em Inglês
| MEDLINE | ID: mdl-32288449
11.
Guidelines for implementation of cystic fibrosis newborn screening programs: Cystic Fibrosis Foundation workshop report.
Pediatrics
; 119(2): e495-518, 2007 Feb.
Artigo
em Inglês
| MEDLINE | ID: mdl-17272609
12.
Newborn screening for cystic fibrosis: an opportunity to improve care and outcomes.
J Pediatr
; 147(3 Suppl): S2-5, 2005 Sep.
Artigo
em Inglês
| MEDLINE | ID: mdl-16202776