Detalhe da pesquisa
1.
Rectal organoid morphology analysis (ROMA) as a promising diagnostic tool in cystic fibrosis.
Thorax
; 76(11): 1146-1149, 2021 11.
Artigo
em Inglês
| MEDLINE | ID: mdl-33859053
2.
Correction of CFTR function in intestinal organoids to guide treatment of cystic fibrosis.
Eur Respir J
; 57(1)2021 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-32747394
3.
Association between faecal pH and fat absorption in children with cystic fibrosis on a controlled diet and enzyme supplements dose.
Pediatr Res
; 89(1): 205-210, 2021 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-32247283
4.
Mucus Release and Airway Constriction by TMEM16A May Worsen Pathology in Inflammatory Lung Disease.
Int J Mol Sci
; 22(15)2021 Jul 22.
Artigo
em Inglês
| MEDLINE | ID: mdl-34360618
5.
Defining Polysaccharide Antibody Deficiency: Measurement of Anti-Pneumococcal Antibodies and Anti-Salmonella typhi Antibodies in a Cohort of Patients with Recurrent Infections.
J Clin Immunol
; 40(1): 105-113, 2020 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-31705452
6.
Cystic fibrosis in the year 2020: A disease with a new face.
Acta Paediatr
; 109(5): 893-899, 2020 05.
Artigo
em Inglês
| MEDLINE | ID: mdl-31899933
7.
Treating the Underlying Cystic Fibrosis Transmembrane Conductance Regulator Defect in Patients with Cystic Fibrosis.
Semin Respir Crit Care Med
; 40(6): 762-774, 2019 12.
Artigo
em Inglês
| MEDLINE | ID: mdl-31659727
8.
Lung function evolution in children with old and new type bronchopulmonary dysplasia: a retrospective cohort analysis.
Eur J Pediatr
; 178(12): 1859-1866, 2019 Dec.
Artigo
em Inglês
| MEDLINE | ID: mdl-31486896
9.
A Method for Comprehensive Proteomic Analysis of Human Faecal Samples to Investigate Gut Dysbiosis in Patients with Cystic Fibrosis.
Adv Exp Med Biol
; 1073: 137-160, 2019.
Artigo
em Inglês
| MEDLINE | ID: mdl-31236842
10.
Lumacaftor-Ivacaftor in Patients with Cystic Fibrosis Homozygous for Phe508del CFTR.
N Engl J Med
; 373(3): 220-31, 2015 07 16.
Artigo
em Inglês
| MEDLINE | ID: mdl-25981758
11.
Diagnosis of Cystic Fibrosis in Nonscreened Populations.
J Pediatr
; 181S: S52-S57.e2, 2017 02.
Artigo
em Inglês
| MEDLINE | ID: mdl-28129813
12.
Cystic fibrosis carriership and tuberculosis: hints toward an evolutionary selective advantage based on data from the Brazilian territory.
BMC Infect Dis
; 17(1): 340, 2017 05 12.
Artigo
em Inglês
| MEDLINE | ID: mdl-28499359
13.
Morphometric Analysis of Explant Lungs in Cystic Fibrosis.
Am J Respir Crit Care Med
; 193(5): 516-26, 2016 Mar 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-26551917
14.
rAAV-CFTRΔR Rescues the Cystic Fibrosis Phenotype in Human Intestinal Organoids and Cystic Fibrosis Mice.
Am J Respir Crit Care Med
; 193(3): 288-98, 2016 Feb 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-26509335
15.
Searching for a cure for cystic fibrosis. A 25-year quest in a nutshell.
Eur J Pediatr
; 175(1): 1-8, 2016 Jan.
Artigo
em Inglês
| MEDLINE | ID: mdl-26567541
16.
Disease-specific clinical trials networks: the example of cystic fibrosis.
Eur J Pediatr
; 175(6): 817-24, 2016 Jun.
Artigo
em Inglês
| MEDLINE | ID: mdl-26979528
17.
Beyond pancreatic insufficiency and liver disease in cystic fibrosis.
Eur J Pediatr
; 175(7): 881-94, 2016 Jul.
Artigo
em Inglês
| MEDLINE | ID: mdl-27055450
18.
A novel translational model for fetoscopic intratracheal delivery of nanoparticles in piglets.
Prenat Diagn
; 36(10): 926-934, 2016 Oct.
Artigo
em Inglês
| MEDLINE | ID: mdl-27567969
19.
Lung structure-function correlation in patients with primary ciliary dyskinesia.
Thorax
; 70(4): 339-45, 2015 Apr.
Artigo
em Inglês
| MEDLINE | ID: mdl-25673230
20.
Lung clearance index predicts pulmonary exacerbations in young patients with cystic fibrosis.
Thorax
; 69(1): 39-45, 2014 Jan.
Artigo
em Inglês
| MEDLINE | ID: mdl-24021874