Detalhe da pesquisa
1.
Efficacy and safety of ivacaftor in patients aged 6 to 11 years with cystic fibrosis with a G551D mutation.
Am J Respir Crit Care Med
; 187(11): 1219-25, 2013 Jun 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-23590265
2.
Effect of VX-770 in persons with cystic fibrosis and the G551D-CFTR mutation.
N Engl J Med
; 363(21): 1991-2003, 2010 Nov 18.
Artigo
em Inglês
| MEDLINE | ID: mdl-21083385
3.
Results of a phase IIa study of VX-809, an investigational CFTR corrector compound, in subjects with cystic fibrosis homozygous for the F508del-CFTR mutation.
Thorax
; 67(1): 12-8, 2012 Jan.
Artigo
em Inglês
| MEDLINE | ID: mdl-21825083
4.
Role of bacteriocins in mediating interactions of bacterial isolates taken from cystic fibrosis patients.
Microbiology (Reading)
; 156(Pt 7): 2058-2067, 2010 Jul.
Artigo
em Inglês
| MEDLINE | ID: mdl-20378653
5.
Genome-wide study of Pseudomonas aeruginosa outer membrane protein immunogenicity using self-assembling protein microarrays.
Infect Immun
; 77(11): 4877-86, 2009 Nov.
Artigo
em Inglês
| MEDLINE | ID: mdl-19737893
6.
Sweat chloride as a biomarker of CFTR activity: proof of concept and ivacaftor clinical trial data.
J Cyst Fibros
; 13(2): 139-47, 2014 Mar.
Artigo
em Inglês
| MEDLINE | ID: mdl-24660233
7.
Optimizing nasal potential difference analysis for CFTR modulator development: assessment of ivacaftor in CF subjects with the G551D-CFTR mutation.
PLoS One
; 8(7): e66955, 2013.
Artigo
em Inglês
| MEDLINE | ID: mdl-23922647
8.
Ivacaftor in subjects with cystic fibrosis who are homozygous for the F508del-CFTR mutation.
Chest
; 142(3): 718-724, 2012 Sep.
Artigo
em Inglês
| MEDLINE | ID: mdl-22383668
9.
A virulence locus of Pseudomonas aeruginosa encodes a protein secretion apparatus.
Science
; 312(5779): 1526-30, 2006 Jun 09.
Artigo
em Inglês
| MEDLINE | ID: mdl-16763151
10.
The treatment of spine and chest wall deformities with fused ribs by expansion thoracostomy and insertion of vertical expandable prosthetic titanium rib: growth of thoracic spine and improvement of lung volumes.
Spine (Phila Pa 1976)
; 30(17 Suppl): S58-68, 2005 Sep 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-16138067
11.
The role of epitope specificity in the human opsonic antibody response to the staphylococcal surface polysaccharide poly N-acetyl glucosamine.
J Infect Dis
; 192(11): 2012-9, 2005 Dec 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-16267775
12.
Variability of markers of inflammation and infection in induced sputum in children with cystic fibrosis.
J Pediatr
; 145(5): 689-92, 2004 Nov.
Artigo
em Inglês
| MEDLINE | ID: mdl-15520781
13.
Inflammatory and microbiologic markers in induced sputum after intravenous antibiotics in cystic fibrosis.
Am J Respir Crit Care Med
; 168(12): 1471-5, 2003 Dec 15.
Artigo
em Inglês
| MEDLINE | ID: mdl-12969869