Detalhe da pesquisa
1.
Use of 2,6-diaminopurine as a potent suppressor of UGA premature stop codons in cystic fibrosis.
Mol Ther
; 31(4): 970-985, 2023 04 05.
Artigo
em Inglês
| MEDLINE | ID: mdl-36641622
2.
High Frequency of Specific Polysaccharide Antibody Deficiency in Adults With Unexplained, Recurrent and/or Severe Infections With Encapsulated Bacteria.
Clin Infect Dis
; 76(5): 800-808, 2023 03 04.
Artigo
em Inglês
| MEDLINE | ID: mdl-36285530
3.
Comparison of Continuous Glucose Monitoring in Cystic Fibrosis Patients With or Without Pancreatic Exocrine Insufficiency.
Horm Metab Res
; 54(6): 407-412, 2022 06.
Artigo
em Inglês
| MEDLINE | ID: mdl-35272389
4.
Rapid Improvement after Starting Elexacaftor-Tezacaftor-Ivacaftor in Patients with Cystic Fibrosis and Advanced Pulmonary Disease.
Am J Respir Crit Care Med
; 204(1): 64-73, 2021 07 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-33600738
5.
Real-Life Safety and Effectiveness of Lumacaftor-Ivacaftor in Patients with Cystic Fibrosis.
Am J Respir Crit Care Med
; 201(2): 188-197, 2020 01 15.
Artigo
em Inglês
| MEDLINE | ID: mdl-31601120
6.
Fertility of women with cystic fibrosis: a French survey.
Reprod Biomed Online
; 39(3): 492-495, 2019 Sep.
Artigo
em Inglês
| MEDLINE | ID: mdl-31256948
7.
Toward the Standardization of Mycological Examination of Sputum Samples in Cystic Fibrosis: Results from a French Multicenter Prospective Study.
Mycopathologia
; 183(1): 101-117, 2018 Feb.
Artigo
em Inglês
| MEDLINE | ID: mdl-28748285
8.
Determinants of exercise capacity in cystic fibrosis patients with mild-to-moderate lung disease.
BMC Pulm Med
; 14: 74, 2014 Apr 30.
Artigo
em Inglês
| MEDLINE | ID: mdl-24884656
9.
Early glucose abnormalities revealed by continuous glucose monitoring associate with lung function decline in cystic fibrosis: A five-year prospective study.
J Diabetes Complications
; 38(4): 108703, 2024 04.
Artigo
em Inglês
| MEDLINE | ID: mdl-38430625
10.
Haemodynamically proven pulmonary hypertension in a patient with GATA2 deficiency-associated pulmonary alveolar proteinosis and fibrosis.
Eur Respir J
; 49(5)2017 05.
Artigo
em Inglês
| MEDLINE | ID: mdl-28495695
11.
Safety and pharmacokinetics of Roscovitine (Seliciclib) in cystic fibrosis patients chronically infected with Pseudomonas aeruginosa, a randomized, placebo-controlled study.
J Cyst Fibros
; 21(3): 529-536, 2022 05.
Artigo
em Inglês
| MEDLINE | ID: mdl-34961705
12.
Clinical response to lumacaftor-ivacaftor in patients with cystic fibrosis according to baseline lung function.
J Cyst Fibros
; 20(2): 220-227, 2021 03.
Artigo
em Inglês
| MEDLINE | ID: mdl-32591294
13.
Predictors of massive haemoptysis after a first episode of mild-to-moderate haemoptysis in patients with cystic fibrosis.
ERJ Open Res
; 6(3)2020 Jul.
Artigo
em Inglês
| MEDLINE | ID: mdl-32963988
14.
First Wave of COVID-19 in French Patients with Cystic Fibrosis.
J Clin Med
; 9(11)2020 Nov 10.
Artigo
em Inglês
| MEDLINE | ID: mdl-33182847
15.
Impact of Achromobacter xylosoxidans isolation on the respiratory function of adult patients with cystic fibrosis.
ERJ Open Res
; 5(4)2019 Oct.
Artigo
em Inglês
| MEDLINE | ID: mdl-31832429
16.
The immediate effects of a single autogenic drainage session on ventilatory mechanics in adult subjects with cystic fibrosis.
PLoS One
; 13(3): e0195154, 2018.
Artigo
em Inglês
| MEDLINE | ID: mdl-29596479
17.
Pulmonary hemorrhage in a neonate born to a woman with cystic fibrosis treated with targeted cystic fibrosis transmembrane conductance regulator modulator elexacaftor-tezacaftor-ivacaftor during pregnancy.
Therapie
; 77(6): 743-745, 2022.
Artigo
em Inglês
| MEDLINE | ID: mdl-35606190
18.
Omalizumab treatment for allergic bronchopulmonary aspergillosis in young patients with cystic fibrosis.
Respir Med
; 133: 12-15, 2017 12.
Artigo
em Inglês
| MEDLINE | ID: mdl-29173443
19.
Optimized approach for the identification of highly efficient correctors of nonsense mutations in human diseases.
PLoS One
; 12(11): e0187930, 2017.
Artigo
em Inglês
| MEDLINE | ID: mdl-29131862
20.
Real-life initiation of lumacaftor/ivacaftor combination in adults with cystic fibrosis homozygous for the Phe508del CFTR mutation and severe lung disease.
J Cyst Fibros
; 16(3): 388-391, 2017 May.
Artigo
em Inglês
| MEDLINE | ID: mdl-28325531