Detalhe da pesquisa
1.
Antioxidants Prevent Iron Accumulation and Lipid Peroxidation, but Do Not Correct Autophagy Dysfunction or Mitochondrial Bioenergetics in Cellular Models of BPAN.
Int J Mol Sci
; 24(19)2023 Sep 26.
Artigo
em Inglês
| MEDLINE | ID: mdl-37834028
2.
Vitamin E prevents lipid peroxidation and iron accumulation in PLA2G6-Associated Neurodegeneration.
Neurobiol Dis
; 165: 105649, 2022 04.
Artigo
em Inglês
| MEDLINE | ID: mdl-35122944
3.
The non-canonical Wnt-PCP pathway shapes the mouse caudal neural plate.
Development
; 145(9)2018 05 08.
Artigo
em Inglês
| MEDLINE | ID: mdl-29636380
4.
Coenzyme Q10: Novel Formulations and Medical Trends.
Int J Mol Sci
; 21(22)2020 Nov 10.
Artigo
em Inglês
| MEDLINE | ID: mdl-33182646
5.
Autophagic dysfunction in patients with Papillon-Lefèvre syndrome is restored by recombinant cathepsin C treatment.
J Allergy Clin Immunol
; 142(4): 1131-1143.e7, 2018 10.
Artigo
em Inglês
| MEDLINE | ID: mdl-29410039
6.
Atherosclerosis and Coenzyme Q10.
Int J Mol Sci
; 20(20)2019 Oct 20.
Artigo
em Inglês
| MEDLINE | ID: mdl-31635164
7.
Two coffins and a funeral: early or late caspase activation determines two types of apoptosis induced by DNA damaging agents.
Apoptosis
; 22(3): 421-436, 2017 Mar.
Artigo
em Inglês
| MEDLINE | ID: mdl-27943067
8.
Dynamic Reorganization of the Cytoskeleton during Apoptosis: The Two Coffins Hypothesis.
Int J Mol Sci
; 18(11)2017 Nov 11.
Artigo
em Inglês
| MEDLINE | ID: mdl-29137119
9.
Apoptotic cells subjected to cold/warming exposure disorganize apoptotic microtubule network and undergo secondary necrosis.
Apoptosis
; 19(9): 1364-77, 2014 Sep.
Artigo
em Inglês
| MEDLINE | ID: mdl-25027509
10.
Targeted delivery of pharmacological chaperones for Gaucher disease to macrophages by a mannosylated cyclodextrin carrier.
Org Biomol Chem
; 12(14): 2289-301, 2014 Apr 14.
Artigo
em Inglês
| MEDLINE | ID: mdl-24589885
11.
Vicious cycle of lipid peroxidation and iron accumulation in neurodegeneration.
Neural Regen Res
; 18(6): 1196-1202, 2023 Jun.
Artigo
em Inglês
| MEDLINE | ID: mdl-36453394
12.
Alpha-lipoic acid supplementation corrects pathological alterations in cellular models of pantothenate kinase-associated neurodegeneration with residual PANK2 expression levels.
Orphanet J Rare Dis
; 18(1): 80, 2023 04 12.
Artigo
em Inglês
| MEDLINE | ID: mdl-37046296
13.
Actin Polymerization Defects Induce Mitochondrial Dysfunction in Cellular Models of Nemaline Myopathies.
Antioxidants (Basel)
; 12(12)2023 Nov 21.
Artigo
em Inglês
| MEDLINE | ID: mdl-38136143
14.
Secondary coenzyme Q10 deficiency triggers mitochondria degradation by mitophagy in MELAS fibroblasts.
FASEB J
; 25(8): 2669-87, 2011 Aug.
Artigo
em Inglês
| MEDLINE | ID: mdl-21551238
15.
The hypoxic preconditioning agent deferoxamine induces poly(ADP-ribose) polymerase-1-dependent inhibition of the mitochondrial respiratory chain.
Mol Cell Biochem
; 363(1-2): 101-8, 2012 Apr.
Artigo
em Inglês
| MEDLINE | ID: mdl-22147195
16.
Therapeutic approach with commercial supplements for pantothenate kinase-associated neurodegeneration with residual PANK2 expression levels.
Orphanet J Rare Dis
; 17(1): 311, 2022 08 09.
Artigo
em Inglês
| MEDLINE | ID: mdl-35945593
17.
Pantothenate and L-Carnitine Supplementation Improves Pathological Alterations in Cellular Models of KAT6A Syndrome.
Genes (Basel)
; 13(12)2022 12 06.
Artigo
em Inglês
| MEDLINE | ID: mdl-36553567
18.
Pterostilbene in Combination With Mitochondrial Cofactors Improve Mitochondrial Function in Cellular Models of Mitochondrial Diseases.
Front Pharmacol
; 13: 862085, 2022.
Artigo
em Inglês
| MEDLINE | ID: mdl-35370630
19.
Modeling Mitochondrial Encephalomyopathy, Lactic Acidosis, and Stroke-Like Episodes Syndrome Using Patient-Derived Induced Neurons Generated by Direct Reprogramming.
Cell Reprogram
; 24(5): 294-303, 2022 10.
Artigo
em Inglês
| MEDLINE | ID: mdl-35802497
20.
Activation of the Mitochondrial Unfolded Protein Response: A New Therapeutic Target?
Biomedicines
; 10(7)2022 Jul 06.
Artigo
em Inglês
| MEDLINE | ID: mdl-35884915