Detalhe da pesquisa
1.
Antibiotic hypersensitivity in cystic fibrosis - Low frequency of anaphylaxis over 16 000 courses.
Br J Clin Pharmacol
; 88(11): 4845-4853, 2022 11.
Artigo
em Inglês
| MEDLINE | ID: mdl-35671007
2.
Characterization of CFTR mutations in people with cystic fibrosis and severe liver disease who are not eligible for CFTR modulators.
J Cyst Fibros
; 22(2): 263-265, 2023 03.
Artigo
em Inglês
| MEDLINE | ID: mdl-36739240
3.
Does newborn screening influence the young cystic fibrosis cohort included in national registries?
Eur Respir J
; 49(1)2017 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-28077474
4.
Ursodeoxycholic acid and liver disease associated with cystic fibrosis: A multicenter cohort study.
J Cyst Fibros
; 21(2): 220-226, 2022 03.
Artigo
em Inglês
| MEDLINE | ID: mdl-33814323
5.
Factors associated with clinical progression to severe COVID-19 in people with cystic fibrosis: A global observational study.
J Cyst Fibros
; 21(4): e221-e231, 2022 07.
Artigo
em Inglês
| MEDLINE | ID: mdl-35753987
6.
Age at diagnosis and disease progression of cystic fibrosis in an area without newborn screening.
Paediatr Perinat Epidemiol
; 25(3): 298-305, 2011 May.
Artigo
em Inglês
| MEDLINE | ID: mdl-21470269
7.
Parental support for newborn screening for cystic fibrosis.
Acta Paediatr
; 100(2): 209-15, 2011 Feb.
Artigo
em Inglês
| MEDLINE | ID: mdl-20950284
8.
The Effects of Aspergillus fumigatus Colonization on Lung Function in Patients with Cystic Fibrosis.
J Fungi (Basel)
; 7(11)2021 Nov 09.
Artigo
em Inglês
| MEDLINE | ID: mdl-34829231
9.
Clinical characteristics of SARS-CoV-2 infection in children with cystic fibrosis: An international observational study.
J Cyst Fibros
; 20(1): 25-30, 2021 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-33309057
10.
Incidence of SARS-CoV-2 in people with cystic fibrosis in Europe between February and June 2020.
J Cyst Fibros
; 20(4): 566-577, 2021 07.
Artigo
em Inglês
| MEDLINE | ID: mdl-34016559
11.
Factors for severe outcomes following SARS-CoV-2 infection in people with cystic fibrosis in Europe.
ERJ Open Res
; 7(4)2021 Oct.
Artigo
em Inglês
| MEDLINE | ID: mdl-34984210
12.
A 16-year retrospective study on fungal prevalence and diversity in patients with cystic fibrosis: Candida dubliniensis was associated with a decline in lung function.
Int J Infect Dis
; 96: 663-670, 2020 Jul.
Artigo
em Inglês
| MEDLINE | ID: mdl-32450290
13.
The global impact of SARS-CoV-2 in 181 people with cystic fibrosis.
J Cyst Fibros
; 19(6): 868-871, 2020 11.
Artigo
em Inglês
| MEDLINE | ID: mdl-33183965
14.
Mutations in the amiloride-sensitive epithelial sodium channel in patients with cystic fibrosis-like disease.
Hum Mutat
; 30(7): 1093-103, 2009 Jul.
Artigo
em Inglês
| MEDLINE | ID: mdl-19462466
15.
Experiences of Individuals Awaiting Lung Transplantation.
Respir Care
; 63(12): 1535-1540, 2018 Dec.
Artigo
em Inglês
| MEDLINE | ID: mdl-30467225
16.
Effect of allergic bronchopulmonary aspergillosis on FEV1 in children and adolescents with cystic fibrosis: a European Cystic Fibrosis Society Patient Registry analysis.
Arch Dis Child
; 102(8): 742-747, 2017 08.
Artigo
em Inglês
| MEDLINE | ID: mdl-28325727
17.
COVID-19 vaccine prioritisation for people with cystic fibrosis.
J Cyst Fibros
; 20(4): 715-716, 2021 07.
Artigo
em Inglês
| MEDLINE | ID: mdl-33941502
18.
European best practice guidelines for cystic fibrosis neonatal screening.
J Cyst Fibros
; 8(3): 153-73, 2009 May.
Artigo
em Inglês
| MEDLINE | ID: mdl-19246252