Glanzmann's thrombasthenia proposed optimal management during surgery and delivery.
Clin Appl Thromb Hemost
; 9(2): 167-70, 2003 Apr.
Article
em En
| MEDLINE
| ID: mdl-12812388
ABSTRACT
Glanzmann's thrombasthenia (GT) is an autosomal recessive disorder of platelet function. Conventional management is by platelet transfusion, given before invasive interventions. Alloimmunization resulting in platelet refractoriness and an unpredictable response to platelet infusion have provided particular management difficulties in the past. More recently recombinant (r)VIIa (Novoseven) has a valuable role in the treatment of platelet function disorders. Treatment of a patient with GT during two pregnancies and spinal surgery is reported. An algorithm is presented to provide a structured and consistent approach to treatment.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Complicações Hematológicas na Gravidez
/
Trombastenia
/
Proteínas Recombinantes
/
Fator VII
/
Transfusão de Plaquetas
/
Discotomia
/
Parto Obstétrico
/
Trabalho de Parto Induzido
/
Vértebras Lombares
Tipo de estudo:
Etiology_studies
Limite:
Adult
/
Female
/
Humans
/
Pregnancy
Idioma:
En
Ano de publicação:
2003
Tipo de documento:
Article