Acinic cell carcinoma: an unusual cause of bronchial obstruction in a child.
Pediatr Dev Pathol
; 7(5): 521-6, 2004.
Article
em En
| MEDLINE
| ID: mdl-15568215
ABSTRACT
Primary acinic cell carcinomas of the lung are rare tumors, usually presenting in adulthood as parenchymal or endobronchial masses. These lesions are generally recognized by their morphological pattern and the presence of periodic acid-Schiff (PAS)-positive, diastase-resistant cytoplasmic granules. We describe a case of pri-mary acinic cell carcinoma of the bronchus in a 4-year-old girl. The tumor has the typical acinar structuresweakly PAS-positive, diastase-resistant cytoplasmic granules and intra-acinar laminated calcific structures. A lobectomy was done with a clear bronchial resection margin. The child is well with no evidence of recurrence or metastasis 2 years postresection.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Carcinoma Broncogênico
/
Carcinoma de Células Acinares
/
Obstrução das Vias Respiratórias
/
Neoplasias Pulmonares
Tipo de estudo:
Diagnostic_studies
Limite:
Child, preschool
/
Female
/
Humans
Idioma:
En
Ano de publicação:
2004
Tipo de documento:
Article