Secondary systemic lupus erythematosus: an analysis of 4 cases of uncontrolled hereditary angioedema.
Clin Immunol
; 123(1): 14-7, 2007 Apr.
Article
em En
| MEDLINE
| ID: mdl-17098477
ABSTRACT
The association of systemic lupus erythematosus and hereditary angioedema (HAE) has formed the basis of numerous case reports and is hypothesised to result from consumption of complement C4 with consequent impaired clearance of apoptotic cells. We describe the development of frank lupus or lupus-like syndrome in four HAE patients with uncontrolled angioedema and low levels of serum C4. Measures that limit hypocomplementaemia in HAE may reduce the incidence of secondary SLE.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Complemento C4
/
Angioedema
/
Lúpus Eritematoso Sistêmico
Limite:
Adolescent
/
Adult
/
Female
/
Humans
/
Male
/
Middle aged
Idioma:
En
Ano de publicação:
2007
Tipo de documento:
Article