[Primary systemic amyloidosis with exclusive involvement of the tongue as an exceptional cause of dysphagia]. / Amiloidosis primaria AL con afección exclusiva de la lengua como causa excepcional de disfagia.

We present a 73-year-old woman with progressive dysphagia and dysarthria over two years associated with systemic symptoms including weight loss, asthenia and dyspnoea. Biopsy of the tongue demonstrated amyloid AL deposits. The immunohistochemical study showed a notable positiveness to antibodies for L-kappa chains. The patient died 6 months after diagnosis.