[Acute type A aortic dissection with Birt-Hogg-Dubé syndrome; report of a case].
Kyobu Geka
; 67(5): 415-8, 2014 May.
Article
em Ja
| MEDLINE
| ID: mdl-24917291
ABSTRACT
We describe a 76-year-old woman with cardiac tamponade who was admitted to our hospital. She underwent ascending and partial arch aortic replacement to treat acute type A aortic dissection. However, postoperative respiratory failure developed and a chest X-ray revealed right lung pneumothorax. The lung was finally expanded after difficulties with prolonged tube drainage. Chest computed tomography(CT) showed multiple cystic changes in the bilateral lungs. Her sister and her daughter also had a history of spontaneous pneumothorax. We finally diagnosed Birt-Hogg-Dube syndrome after deoxyribonucleic asid(DNA)sequencing of folliculin( FLCN) gene.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Aneurisma da Aorta Torácica
/
Síndrome de Birt-Hogg-Dubé
/
Dissecção Aórtica
Limite:
Aged
/
Female
/
Humans
Idioma:
Ja
Ano de publicação:
2014
Tipo de documento:
Article