Bullous Kaposiform Hemangioendothelioma Masquerading as Aplasia Cutis Congenita.
Pediatr Dermatol
; 33(5): e267-9, 2016 Sep.
Article
em En
| MEDLINE
| ID: mdl-27339319
ABSTRACT
We present the case of a male infant with violaceous bullae on the scalp that were initially thought to be bullous aplasia cutis but at 3 months of age were diagnosed as a kaposiform hemangioendothelioma. This diagnosis should be considered when evaluating newborns with bullous plaques on the scalp that do not heal in the first 2-3 weeks of life. Kaposiform hemangioendothelioma (KHE) is a rare vascular tumor that typically presents as a violaceous to purpuric plaque at birth or early infancy. It may be associated with Kasabach-Merritt phenomenon (KMP), a potentially life-threatening consumptive coagulopathy.
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Sarcoma de Kaposi
/
Couro Cabeludo
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Displasia Ectodérmica
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Síndrome de Kasabach-Merritt
/
Hemangioendotelioma
Tipo de estudo:
Diagnostic_studies
Limite:
Humans
/
Infant
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Male
Idioma:
En
Ano de publicação:
2016
Tipo de documento:
Article