Nasal Fibrolipomatous Hamartoma, an Idiosyncratic Connective Tissue Malformation in an Infant.
Fetal Pediatr Pathol
; 36(1): 76-81, 2017 Feb.
Article
em En
| MEDLINE
| ID: mdl-27629571
We describe a congenital mass in the nasopharynx of an infant presenting with dyspnea and feeding difficulties. Magnetic resonance imaging demonstrated 2 separate polypoid nasal cavity masses that were endoscopically resected. Histologically, both lesions were composed of mature adipose tissue with broad fibrous bands and several foci of brown fat. PLAG-1 and HMGA-2 were negative by immunostains. The best diagnosis was a fibrolipomatous hamartoma.
Palavras-chave
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Proteína HMGA2
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Proteínas de Ligação a DNA
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Hamartoma
Tipo de estudo:
Diagnostic_studies
Limite:
Female
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Humans
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Newborn
Idioma:
En
Ano de publicação:
2017
Tipo de documento:
Article