Outcome of intrahepatic portosystemic shunt diagnosed prenatally.
Eur J Pediatr
; 176(12): 1613-1618, 2017 Dec.
Article
em En
| MEDLINE
| ID: mdl-28913555
ABSTRACT
We analyzed the characteristics of the population with congenital portosystemic shunt diagnosed during the antenatal period and the organization of their perinatal care. This multicentric retrospective study included all the patients with a prenatal diagnosis of congenital portosystemic shunt. Between 1999 and 2015, 12 patients were included. Prenatal diagnosis was done at a median 26.5 weeks of gestation (21-34). All the patients presented intrahepatic CPSS, three of them had associated congenital cardiopathy, and one a Bannayan-Zonana syndrome. Ten patients had simple outcome on conservative treatment, eight of them having a spontaneous closure of their portosystemic shunt within the first 2 years of life. One patient had surgical treatment which failed and he developed a focal nodular hyperplasia. Another patient had radiological interventional closure of his shunt which was complicated by a venal portal thrombosis. CONCLUSION:
Outcome of intrahepatic portosystemic shunt diagnosed prenatally is good in the majority of cases. What is known ⢠Multiples studies exist on congenital porto systemic shunt but when the diagnosis is done after birth. ⢠The evolution, management, and complication are well known. What is new ⢠There is very few studies with only patients diagnosed in antenatal and it is a large series of cases. ⢠Outcome of intrahepatic portosystemic shunt diagnosed prenatally is good in the majority of cases.Palavras-chave
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Veia Porta
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Ultrassonografia Pré-Natal
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Malformações Vasculares
Tipo de estudo:
Diagnostic_studies
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Observational_studies
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Prognostic_studies
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Risk_factors_studies
Limite:
Child
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Child, preschool
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Female
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Humans
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Infant
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Male
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Newborn
Idioma:
En
Ano de publicação:
2017
Tipo de documento:
Article