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Split-graft liver transplantation from an adult donor with an unrecognized UCD to a pediatric and adult recipient.
Lee, C H; Ellaway, C; Shun, A; Thomas, G; Nair, P; O'Neill, J; Shakel, N; Stormon, M O.
Afiliação
  • Lee CH; Department of Gastroenterology and Hepatology, The Children's Hospital at Westmead, Westmead, NSW, Australia.
  • Ellaway C; Genetic Metabolic Disorders Service, The Children's Hospital at Westmead, Westmead, NSW, Australia.
  • Shun A; Department of Surgery, The Children's Hospital at Westmead, Westmead, NSW, Australia.
  • Thomas G; Department of Surgery, The Children's Hospital at Westmead, Westmead, NSW, Australia.
  • Nair P; Intensive Care Unit, St Vincent's Hospital, Sydney, NSW, Australia.
  • O'Neill J; Department of Neurology, St Vincent's Hospital, Sydney, NSW, Australia.
  • Shakel N; Department of Gastroenterology and Hepatology, Royal Prince Alfred Hospital, Sydney, NSW, Australia.
  • Stormon MO; Department of Gastroenterology and Hepatology, The Children's Hospital at Westmead, Westmead, NSW, Australia.
Pediatr Transplant ; 22(1)2018 02.
Article em En | MEDLINE | ID: mdl-29044911
ABSTRACT
We report the outcomes of an adult and pediatric split liver transplant from an adult male donor who died due to an unrecognized UCD, OTC deficiency. Recognizing inborn errors of metabolism can be challenging, especially in adult centers where such disorders are rarely encountered. Shortage of donors for liver transplantation has led to procedures to maximize donor utilization, such as split and live donor grafts. The cause of death should be ascertained before accepting a cadaveric donor organ.
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Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Complicações Pós-Operatórias / Transplante de Fígado / Doença da Deficiência de Ornitina Carbomoiltransferase Tipo de estudo: Etiology_studies Limite: Adult / Child / Female / Humans / Male Idioma: En Ano de publicação: 2018 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Complicações Pós-Operatórias / Transplante de Fígado / Doença da Deficiência de Ornitina Carbomoiltransferase Tipo de estudo: Etiology_studies Limite: Adult / Child / Female / Humans / Male Idioma: En Ano de publicação: 2018 Tipo de documento: Article