World's smallest combined en bloc liver-pancreas transplantation.
Pediatr Transplant
; 22(1)2018 02.
Article
em En
| MEDLINE
| ID: mdl-29139617
ABSTRACT
We present a case of a 2-year-old child who underwent a combined en bloc liver and pancreas transplant following complications of WRS. WRS is characterized clinically through infantile insulin-dependent diabetes mellitus, neutropenia, recurrent infections, propensity for liver failure following viral infections, bone dysplasia, and developmental delay. Usually, death occurs from fulminant liver and concomitant kidney failure. Few cases with WRS are reported in the literature, mostly from consanguineous parents. To the best of our knowledge, combined en bloc liver and pancreas transplant has not been performed in small children.
Palavras-chave
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Osteocondrodisplasias
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Transplante de Fígado
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Transplante de Pâncreas
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Diabetes Mellitus Tipo 1
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Epífises
Limite:
Child, preschool
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Female
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Humans
Idioma:
En
Ano de publicação:
2018
Tipo de documento:
Article