[Kearns-Sayre syndrome: complete auriculoventricular block, torsade de pointes and ventricular fibrillation]. / Syndrome de Kearns-Sayre: bloc auriculo-ventriculaire complet, torsade de pointes et fibrillation ventriculaire.
Ann Cardiol Angeiol (Paris)
; 37(9): 529-34, 1988 Nov.
Article
em Fr
| MEDLINE
| ID: mdl-3066274
ABSTRACT
The authors present the case of a new case of Kearns-Sayre syndrome, with early manifestations (7 months) and dramatic cardiac course. They document the ultimate and often fatal stage of the cardiac disorders of this syndrome, which was usually related to an asystole due to a total atrio-ventricular block and represented in this case by a ventricular hyperexcitability (ventricular tachycardia--"torsade de pointes"--ventricular fibrillation) occurring on an atrio-ventricular block; only one previous, undocumented case was found in the literature. The literature is reviewed in order to analyze the nature and chronology of the heart disorders in the course of the disease, and stress the screening modalities and therapeutic indications (continuous heart stimulation).
Buscar no Google
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Taquicardia
/
Fibrilação Ventricular
/
Oftalmoplegia
/
Síndrome de Kearns-Sayre
/
Bloqueio Cardíaco
Tipo de estudo:
Prognostic_studies
Limite:
Humans
/
Infant
/
Male
Idioma:
Fr
Ano de publicação:
1988
Tipo de documento:
Article