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Early myopathy in Duchenne muscular dystrophy is associated with elevated mitochondrial H2 O2 emission during impaired oxidative phosphorylation.
Hughes, Meghan C; Ramos, Sofhia V; Turnbull, Patrick C; Rebalka, Irena A; Cao, Andrew; Monaco, Cynthia M F; Varah, Nina E; Edgett, Brittany A; Huber, Jason S; Tadi, Peyman; Delfinis, Luca J; Schlattner, U; Simpson, Jeremy A; Hawke, Thomas J; Perry, Christopher G R.
Afiliação
  • Hughes MC; School of Kinesiology and Health Science, Muscle Health Research Centre, 344 Norman Bethune College, York University, Toronto, ON, Canada.
  • Ramos SV; School of Kinesiology and Health Science, Muscle Health Research Centre, 344 Norman Bethune College, York University, Toronto, ON, Canada.
  • Turnbull PC; School of Kinesiology and Health Science, Muscle Health Research Centre, 344 Norman Bethune College, York University, Toronto, ON, Canada.
  • Rebalka IA; Department of Pathology and Molecular Medicine, McMaster University, Hamilton, ON, Canada.
  • Cao A; Department of Pathology and Molecular Medicine, McMaster University, Hamilton, ON, Canada.
  • Monaco CMF; Department of Pathology and Molecular Medicine, McMaster University, Hamilton, ON, Canada.
  • Varah NE; Department of Pathology and Molecular Medicine, McMaster University, Hamilton, ON, Canada.
  • Edgett BA; Department of Human Health and Nutritional Sciences and Cardiovascular Research Group, University of Guelph, Guelph, ON, Canada.
  • Huber JS; Department of Human Health and Nutritional Sciences and Cardiovascular Research Group, University of Guelph, Guelph, ON, Canada.
  • Tadi P; School of Kinesiology and Health Science, Muscle Health Research Centre, 344 Norman Bethune College, York University, Toronto, ON, Canada.
  • Delfinis LJ; School of Kinesiology and Health Science, Muscle Health Research Centre, 344 Norman Bethune College, York University, Toronto, ON, Canada.
  • Schlattner U; Laboratory of Fundamental and Applied Bioenergetics (LBFA) and SFR Environmental and Systems Biology (BEeSy), University Grenoble Alpes, Grenoble, France.
  • Simpson JA; Department of Human Health and Nutritional Sciences and Cardiovascular Research Group, University of Guelph, Guelph, ON, Canada.
  • Hawke TJ; Department of Pathology and Molecular Medicine, McMaster University, Hamilton, ON, Canada.
  • Perry CGR; School of Kinesiology and Health Science, Muscle Health Research Centre, 344 Norman Bethune College, York University, Toronto, ON, Canada.
J Cachexia Sarcopenia Muscle ; 10(3): 643-661, 2019 06.
Article em En | MEDLINE | ID: mdl-30938481

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Músculo Esquelético / Distrofia Muscular de Duchenne / Complexo I de Transporte de Elétrons / Peróxido de Hidrogênio / Mitocôndrias Tipo de estudo: Risk_factors_studies Limite: Animals / Humans / Male Idioma: En Ano de publicação: 2019 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Músculo Esquelético / Distrofia Muscular de Duchenne / Complexo I de Transporte de Elétrons / Peróxido de Hidrogênio / Mitocôndrias Tipo de estudo: Risk_factors_studies Limite: Animals / Humans / Male Idioma: En Ano de publicação: 2019 Tipo de documento: Article