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Glutamine Synthetase 1 Increases Autophagy Lysosomal Degradation of Mutant Huntingtin Aggregates in Neurons, Ameliorating Motility in a Drosophila Model for Huntington's Disease.
Vernizzi, Luisa; Paiardi, Chiara; Licata, Giusimaria; Vitali, Teresa; Santarelli, Stefania; Raneli, Martino; Manelli, Vera; Rizzetto, Manuela; Gioria, Mariarosa; Pasini, Maria E; Grifoni, Daniela; Vanoni, Maria A; Gellera, Cinzia; Taroni, Franco; Bellosta, Paola.
Afiliação
  • Vernizzi L; Department of Biosciences, University of Milan, 20133 Milan, Italy.
  • Paiardi C; Department of Biosciences, University of Milan, 20133 Milan, Italy.
  • Licata G; Department of Biosciences, University of Milan, 20133 Milan, Italy.
  • Vitali T; Department of Biosciences, University of Milan, 20133 Milan, Italy.
  • Santarelli S; Department of Cellular, Computational and Integrative Biology (CiBio), University of Trento, 38123 Trento, Italy.
  • Raneli M; Department of Biosciences, University of Milan, 20133 Milan, Italy.
  • Manelli V; Department of Biosciences, University of Milan, 20133 Milan, Italy.
  • Rizzetto M; Unit of Medical Genetics and Neurogenetics, Fondazione IRCCS Istituto Neurologico Carlo Besta, 20133 Milan, Italy.
  • Gioria M; Department of Biosciences, University of Milan, 20133 Milan, Italy.
  • Pasini ME; Department of Biosciences, University of Milan, 20133 Milan, Italy.
  • Grifoni D; Department of Pharmacy and Biotechnology, University of Bologna, 40126 Bologna, Italy.
  • Vanoni MA; Department of Biosciences, University of Milan, 20133 Milan, Italy.
  • Gellera C; Unit of Medical Genetics and Neurogenetics, Fondazione IRCCS Istituto Neurologico Carlo Besta, 20133 Milan, Italy.
  • Taroni F; Unit of Medical Genetics and Neurogenetics, Fondazione IRCCS Istituto Neurologico Carlo Besta, 20133 Milan, Italy.
  • Bellosta P; Department of Biosciences, University of Milan, 20133 Milan, Italy.
Cells ; 9(1)2020 01 13.
Article em En | MEDLINE | ID: mdl-31941072

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Autofagia / Doença de Huntington / Modelos Animais de Doenças / Glutamato-Amônia Ligase / Lisossomos / Neurônios Limite: Animals Idioma: En Ano de publicação: 2020 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Autofagia / Doença de Huntington / Modelos Animais de Doenças / Glutamato-Amônia Ligase / Lisossomos / Neurônios Limite: Animals Idioma: En Ano de publicação: 2020 Tipo de documento: Article