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Deficiency of 3-hydroxybutyrate dehydrogenase (BDH1) in mice causes low ketone body levels and fatty liver during fasting.
Otsuka, Hiroki; Kimura, Takeshi; Ago, Yasuhiko; Nakama, Mina; Aoyama, Yuka; Abdelkreem, Elsayed; Matsumoto, Hideki; Ohnishi, Hidenori; Sasai, Hideo; Osawa, Masatake; Yamaguchi, Seiji; Mitchell, Grant A; Fukao, Toshiyuki.
Afiliação
  • Otsuka H; Department of Pediatrics, Graduate School of Medicine, Gifu University, Gifu City, Japan.
  • Kimura T; Department of Neonatology, Gifu Prefectural General Medical Center, Gifu City, Japan.
  • Ago Y; Department of Pediatrics, Graduate School of Medicine, Gifu University, Gifu City, Japan.
  • Nakama M; Department of Pediatrics, Graduate School of Medicine, Gifu University, Gifu City, Japan.
  • Aoyama Y; Clinical Genetics Center, Gifu University Hospital, Gifu City, Japan.
  • Abdelkreem E; Department of Pediatrics, Graduate School of Medicine, Gifu University, Gifu City, Japan.
  • Matsumoto H; Department of Biomedical Sciences, College of Life and Health Sciences, Education and Training Center of Medical Technology, Chubu University, Kasugai City, Japan.
  • Ohnishi H; Department of Pediatrics, Graduate School of Medicine, Gifu University, Gifu City, Japan.
  • Sasai H; Department of Pediatrics, Faculty of Medicine, Sohag University, Nasser City, Egypt.
  • Osawa M; Department of Pediatrics, Graduate School of Medicine, Gifu University, Gifu City, Japan.
  • Yamaguchi S; Department of Pediatrics, Graduate School of Medicine, Gifu University, Gifu City, Japan.
  • Mitchell GA; Department of Pediatrics, Graduate School of Medicine, Gifu University, Gifu City, Japan.
  • Fukao T; Clinical Genetics Center, Gifu University Hospital, Gifu City, Japan.
J Inherit Metab Dis ; 43(5): 960-968, 2020 09.
Article em En | MEDLINE | ID: mdl-32279332

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Jejum / Fígado Gorduroso / Hidroxibutirato Desidrogenase / Corpos Cetônicos / Fígado Tipo de estudo: Etiology_studies Limite: Animals Idioma: En Ano de publicação: 2020 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Jejum / Fígado Gorduroso / Hidroxibutirato Desidrogenase / Corpos Cetônicos / Fígado Tipo de estudo: Etiology_studies Limite: Animals Idioma: En Ano de publicação: 2020 Tipo de documento: Article