Case series of three adult patients with exceptional clinical presentations of haemophagocytic lymphohistiocytosis.
Neth J Med
; 78(3): 136-141, 2020 04.
Article
em En
| MEDLINE
| ID: mdl-32332189
ABSTRACT
Macrophage activation syndrome (MAS) is a secondary form of haemophagocytic lymphohistiocytosis (HLH). MAS-HLH is an underrecognised and life-threatening condition associated with a heterogeneous group of diseases including connective tissue disease and inflammatory disorders. Here, we report three cases of adult patients with MAS-HLH triggered by different entities, including systemic lupus erythematosus, Griscelli syndrome type 2, and Adult onset Still's disease.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Piebaldismo
/
Doença de Still de Início Tardio
/
Linfo-Histiocitose Hemofagocítica
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Síndrome de Ativação Macrofágica
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Doenças da Imunodeficiência Primária
/
Lúpus Eritematoso Sistêmico
Limite:
Adult
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Female
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Humans
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Male
/
Middle aged
Idioma:
En
Ano de publicação:
2020
Tipo de documento:
Article