Muscle Tone Assessment under General Anesthesia for Sjögren-Larsson Syndrome and Spasticity.
Pediatr Neurosurg
; 56(2): 163-165, 2021.
Article
em En
| MEDLINE
| ID: mdl-33725695
ABSTRACT
INTRODUCTION:
Study of muscle tone in individuals with severe spasticity (Modified Asworth Scale - MAS3) under general anesthesia can confirm or rule out the eventual necessity of the impending spasticity relieving ablative neurosurgery by observing the hypertonia reduction and passive range of motion expansion. Therefore, what we measure under muscle relaxants is practically a fixed deformity. CASE PRESENTATION The study was performed on a girl with Sjögren-Larsson syndrome, presenting with icthyosis and spastic diplegia. Proposed intervention was Dorsal Rhizotomy. Under general anesthesia, with and without muscle relaxants, hypertonia was significantly reduced (MAS1), but the angle of motion did not increase much.CONCLUSION:
We decided not to perform such a neurosurgical procedure. In ambiguous situations, the proposed study can help in decision-making for spasticity treatment.Palavras-chave
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Paralisia Cerebral
/
Síndrome de Sjogren-Larsson
Tipo de estudo:
Prognostic_studies
Limite:
Female
/
Humans
Idioma:
En
Ano de publicação:
2021
Tipo de documento:
Article