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Acitretin mitigates uroporphyrin-induced bone defects in congenital erythropoietic porphyria models.
Bragazzi Cunha, Juliana; Elenbaas, Jared S; Maitra, Dhiman; Kuo, Ning; Azuero-Dajud, Rodrigo; Ferguson, Allison C; Griffin, Megan S; Lentz, Stephen I; Shavit, Jordan A; Omary, M Bishr.
Afiliação
  • Bragazzi Cunha J; Center for Advanced Biotechnology and Medicine, Rutgers University, Piscataway, 08854, USA. bragazzi@umich.edu.
  • Elenbaas JS; Medical Scientist Training Program, Washington University, Saint Louis, 63110, USA.
  • Maitra D; Center for Advanced Biotechnology and Medicine, Rutgers University, Piscataway, 08854, USA.
  • Kuo N; Center for Advanced Biotechnology and Medicine, Rutgers University, Piscataway, 08854, USA.
  • Azuero-Dajud R; Center for Advanced Biotechnology and Medicine, Rutgers University, Piscataway, 08854, USA.
  • Ferguson AC; Department of Pediatrics, Division of Pediatric Hematology/Oncology, University of Michigan, Ann Arbor, 48109, USA.
  • Griffin MS; Department of Pediatrics, Division of Pediatric Hematology/Oncology, University of Michigan, Ann Arbor, 48109, USA.
  • Lentz SI; Department of Internal Medicine, Division of Metabolism, Endocrinology and Diabetes, University of Michigan, Ann Arbor, 48109, USA.
  • Shavit JA; Department of Pediatrics, Division of Pediatric Hematology/Oncology, University of Michigan, Ann Arbor, 48109, USA.
  • Omary MB; Center for Advanced Biotechnology and Medicine, Rutgers University, Piscataway, 08854, USA. bo163@cabm.rutgers.edu.
Sci Rep ; 11(1): 9601, 2021 05 05.
Article em En | MEDLINE | ID: mdl-33953217

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Uroporfirinas / Osso e Ossos / Desenvolvimento Ósseo / Porfiria Eritropoética / Acitretina Tipo de estudo: Prognostic_studies Limite: Animals Idioma: En Ano de publicação: 2021 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Uroporfirinas / Osso e Ossos / Desenvolvimento Ósseo / Porfiria Eritropoética / Acitretina Tipo de estudo: Prognostic_studies Limite: Animals Idioma: En Ano de publicação: 2021 Tipo de documento: Article