Primary Intracerebral Alveolar Soft Part Sarcoma: Report of a Case and Review of the Literature.
Int J Surg Pathol
; 30(2): 195-199, 2022 Apr.
Article
em En
| MEDLINE
| ID: mdl-34142883
ABSTRACT
Alveolar soft part sarcomas (ASPSs) are rare malignant tumors representing â¼1% of all soft tissue sarcomas. Most ASPS occurring in the central nervous system are metastases. In contrast, primary intracranial ASPSs are extremely rare and only 8 cases have been previously reported in English literature. Here, we report a case of primary alveolar soft part sarcoma in a 16-year-old female patient with no evidence of primary extracranial tumors. Histologically this case fulfilled the criteria of ASPS, and a molecular confirmation has been archived. To date, only 9 primary intracranial ASPS cases, including ours, have been reported in the literature. This report highlights the clinical and pathological characteristics, differential diagnosis, and molecular analysis of primary ASPS of the central nervous system.
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Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Neoplasias de Tecidos Moles
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Sarcoma Alveolar de Partes Moles
Tipo de estudo:
Diagnostic_studies
/
Systematic_reviews
Limite:
Adolescent
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Female
/
Humans
Idioma:
En
Ano de publicação:
2022
Tipo de documento:
Article