Inflammatory myophibroblastic tumor of the proximal ileon in a patient with complicated umbilical hernia: A case report and literature review.

ABSTRACT

INTRODUCTION: Inflammatory myofibroblastic tumors are neoplasms that occur infrequently, mainly affects children and young adults. It is an intermediate grade fibrotic multinodular neoplasm. DESCRIPTION OF THE CASE We present the case of a 47-year-old female patient, who underwent emergency umbilical hernioplasty, later developed intestinal obstruction secondary to an inflammatory myofibroblastic tumor. DISCUSSION: In 1939 Brunn described it for the first time, later in 1954 Umiker named it "Inflammatory Myofibroblastic Tumor". The symptoms are nonspecific. In 15 to 40% of patients they are asymptomatic. Cells positive for actin, smooth muscle, vimentin and desmin, in 3367% of cases the cells are positive for ALK, which is present in some malignant lesions. The recommended treatment is radical resection. CONCLUSION: The diagnosis is established by histopathological study, surgery is the cornerstone of treatment.