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Defects in mucosal immunity and nasopharyngeal dysbiosis in HSC-transplanted SCID patients with IL2RG/JAK3 deficiency.
Goncalves, Pedro; Doisne, Jean-Marc; Eri, Toshiki; Charbit, Bruno; Bondet, Vincent; Posseme, Celine; Llibre, Alba; Casrouge, Armanda; Lenoir, Christelle; Neven, Bénédicte; Duffy, Darragh; Fischer, Alain; Di Santo, James P.
Afiliação
  • Goncalves P; Institut Pasteur, Université de Paris Cité, Inserm U1223, Innate Immunity Unit, Paris, France.
  • Doisne JM; Institut Pasteur, Université de Paris Cité, Inserm U1223, Innate Immunity Unit, Paris, France.
  • Eri T; Institut Pasteur, Université de Paris Cité, Inserm U1223, Innate Immunity Unit, Paris, France.
  • Charbit B; Institut Pasteur, Université de Paris Cité, Center for Translational Science, Paris, France.
  • Bondet V; Institut Pasteur, Université de Paris Cité, Translational Immunology Unit, Paris, France.
  • Posseme C; Institut Pasteur, Université de Paris Cité, Translational Immunology Unit, Paris, France.
  • Llibre A; Institut Pasteur, Université de Paris Cité, Translational Immunology Unit, Paris, France.
  • Casrouge A; Institut Pasteur, Université de Paris Cité, Inserm U1223, Innate Immunity Unit, Paris, France.
  • Lenoir C; Inserm Unité Mixte de Recherche 1163, Paris, France.
  • Neven B; Imagine Institut, Université de Paris Descartes Sorbonne Paris Cité, Paris, France.
  • Duffy D; Inserm Unité Mixte de Recherche 1163, Paris, France.
  • Fischer A; Imagine Institut, Université de Paris Descartes Sorbonne Paris Cité, Paris, France.
  • Di Santo JP; Department of Pediatric Immunology, Hematology and Rheumatology, Hôpital Necker-Enfants Malades, Assistance Publique-Hôpitaux de Paris, Paris, France; and.
Blood ; 139(17): 2585-2600, 2022 04 28.
Article em En | MEDLINE | ID: mdl-35157765

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Imunodeficiência Combinada Severa Limite: Humans Idioma: En Ano de publicação: 2022 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Imunodeficiência Combinada Severa Limite: Humans Idioma: En Ano de publicação: 2022 Tipo de documento: Article