ANCA-Associated Vasculitis in a Patient with Chronic Thromboembolic Pulmonary Hypertension.
Tokai J Exp Clin Med
; 47(1): 26-30, 2022 Apr 20.
Article
em En
| MEDLINE
| ID: mdl-35383867
ABSTRACT
An 82-year-old woman with a history of chronic thromboembolic pulmonary hypertension (CTEPH) presented with malaise, left facial nerve paralysis and the positive seroconversion of myeloperoxidase (MPO)-antineutrophil cytoplasmic antibody (ANCA). She was diagnosed with ANCA-associated vasculitis (AAV). Administration of corticosteroids significantly improved her symptoms, with a decline in the serum MPOANCA level. Ten months later than the initial presentation, she developed an AAV exacerbation with lung infiltration and pericardial effusion, which improved with high-dose corticosteroid therapy. To date, a limited number of AAV cases concomitant with pulmonary hypertension have been reported. The case report presented herein suggests a potential role for CTEPH in the development of AAV.
Buscar no Google
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Vasculite Associada a Anticorpo Anticitoplasma de Neutrófilos
/
Hipertensão Pulmonar
Tipo de estudo:
Etiology_studies
/
Risk_factors_studies
Limite:
Aged80
/
Female
/
Humans
Idioma:
En
Ano de publicação:
2022
Tipo de documento:
Article