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Nutritional co-therapy with 1,3-butanediol and multi-ingredient antioxidants enhances autophagic clearance in Pompe disease.
Nilsson, Mats I; Crozier, Michael; Di Carlo, Alessia; Xhuti, Donald; Manta, Katherine; Roik, Liza J; Bujak, Adam L; Nederveen, Joshua P; Tarnopolsky, Milla G; Hettinga, Bart; Meena, Naresh K; Raben, Nina; Tarnopolsky, Mark A.
Afiliação
  • Nilsson MI; Department of Pediatrics, McMaster University, Hamilton, Ontario, Canada; Exerkine Corporation, McMaster University, Hamilton, Ontario, Canada.
  • Crozier M; Department of Pediatrics, McMaster University, Hamilton, Ontario, Canada.
  • Di Carlo A; Department of Pediatrics, McMaster University, Hamilton, Ontario, Canada.
  • Xhuti D; Exerkine Corporation, McMaster University, Hamilton, Ontario, Canada.
  • Manta K; Department of Pediatrics, McMaster University, Hamilton, Ontario, Canada.
  • Roik LJ; Department of Pediatrics, McMaster University, Hamilton, Ontario, Canada.
  • Bujak AL; Department of Pediatrics, McMaster University, Hamilton, Ontario, Canada.
  • Nederveen JP; Department of Pediatrics, McMaster University, Hamilton, Ontario, Canada.
  • Tarnopolsky MG; Department of Pediatrics, McMaster University, Hamilton, Ontario, Canada.
  • Hettinga B; Exerkine Corporation, McMaster University, Hamilton, Ontario, Canada.
  • Meena NK; Cell and Developmental Biology Center, National Heart, Lung, and Blood Institute, NIH, Bethesda, MD, USA.
  • Raben N; Cell and Developmental Biology Center, National Heart, Lung, and Blood Institute, NIH, Bethesda, MD, USA.
  • Tarnopolsky MA; Department of Pediatrics, McMaster University, Hamilton, Ontario, Canada; Exerkine Corporation, McMaster University, Hamilton, Ontario, Canada. Electronic address: tarnopol@mcmaster.ca.
Mol Genet Metab ; 137(1-2): 228-240, 2022.
Article em En | MEDLINE | ID: mdl-35718712

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Doença de Depósito de Glicogênio Tipo II / Ácido Tióctico Limite: Animals Idioma: En Ano de publicação: 2022 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Doença de Depósito de Glicogênio Tipo II / Ácido Tióctico Limite: Animals Idioma: En Ano de publicação: 2022 Tipo de documento: Article