Cochlear implantation in a profoundly deaf child with cystic leukoencephalopathy without megalencephaly.
J Laryngol Otol
; 137(5): 584-587, 2023 May.
Article
em En
| MEDLINE
| ID: mdl-35979751
ABSTRACT
BACKGROUND:
Cochlear implantation candidacy criteria have continued to evolve over the years, and cochlear implantation is possible with many inner-ear and brain anomalies with good hearing and linguistic outcomes. Cystic leukoencephalopathy without megalencephaly is a rare disease in children, with only 30 cases reported in the literature, but it is associated with hearing loss in only three cases. Radiological investigations can help in diagnosing this rare entity before proceeding with cochlear implantation. CASE REPORT A four-year-old female child born out of consanguinity with normal psychomotor development, bilateral sensorineural hearing loss and an incidental magnetic resonance imaging finding of cystic leukoencephalopathy without megalencephaly underwent successful cochlear implantation. Her post-operative period was uneventful with successful mapping of the cochlear implant.CONCLUSION:
This is the first reported case of cystic leukoencephalopathy without megalencephaly and with sensorineural hearing loss in which cochlear implantation was performed successfully. White matter and temporal lobe abnormalities should not deter paediatric cochlear implantation.Palavras-chave
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Implantes Cocleares
/
Implante Coclear
/
Leucoencefalopatias
/
Megalencefalia
/
Perda Auditiva Neurossensorial
Limite:
Child
/
Child, preschool
/
Female
/
Humans
Idioma:
En
Ano de publicação:
2023
Tipo de documento:
Article