[Atypical chest pain revealing an asymptomatic Ebstein´s anomaly: case report]. / Une maladie d'Ebstein asymptomatique découverte à l'occasion d'une douleur thoracique atypique: à propos d'un cas.

ABSTRACT

Ebstein´s disease is a rare congenital malformation whose clinical presentation differs according to the anatomical form and age of the patient. In adults, it presents mainly as right or global heart failure or arrhythmia. Survival is exceptionally long in some cases. Management varies according to the anatomical form and clinical presentation, ranging from simple surveillance for asymptomatic patients to surgical management for other cases. We report the case of a patient with asymptomatic Ebstein´s disease until the age of 54 years when it was discovered at the time of atypical chest pain, an uncommon presentation of the disease. Management in this case consisted of strict clinical and ultrasound surveillance.