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Isolated left ventricular apical hypoplasia: case report.
Román, Ricardo; Anchante, Henry; Menacho, Katia; Medina, Félix.
Afiliação
  • Román R; Division of Cardiology, Cayetano Heredia Hospital, San Martin de Porres, Lima 15102, Perú.
  • Anchante H; Division of Cardiology, Cayetano Heredia Hospital, San Martin de Porres, Lima 15102, Perú.
  • Menacho K; Barts Heart Centre, St Bartholomew's Hospital, W Smithfield, London EC1A 7BE, UK.
  • Medina F; Division of Cardiology, Cayetano Heredia Hospital, San Martin de Porres, Lima 15102, Perú.
Eur Heart J Case Rep ; 7(2): ytad046, 2023 Feb.
Article em En | MEDLINE | ID: mdl-36845834
ABSTRACT

Background:

Isolated left ventricular apical hypoplasia (ILVAH) is a rare, probably congenital, cardiac condition recently reported in the last two decades. Although most cases are asymptomatic or mildly symptomatic, some severe and fatal cases have been reported, leading to more efforts for appropriate diagnosis and treatment. We describe the first, and severe, case of this pathology in Peru and Latin America. Case

summary:

A 24-year-old male with a history of long-standing alcohol and illicit drug use presented with symptoms of heart failure (HF) and atrial fibrillation (AF). Transthoracic echocardiography showed biventricular dysfunction along with spherical left ventricle, abnormal papillary muscles' origin from the left ventricular apex, and an elongated right ventricle wrapping around the deficient left ventricular apex. Cardiac magnetic resonance confirmed these findings and revealed subepicardial fatty replacement at the left ventricular apex. The diagnosis of ILVAH was made. He was discharged from hospital with carvedilol, enalapril, digoxin, and warfarin. Eighteen months later he remains mildly symptomatic at New York Heart Association functional class II without worsening HF nor thrombo-embolism.

Discussion:

This case highlights the usefulness of multimodality non-invasive cardiovascular imaging for accurate diagnosis of ILVAH as well as the importance of close follow-up and treatment of established complications (HF and AF).
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Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Idioma: En Ano de publicação: 2023 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Idioma: En Ano de publicação: 2023 Tipo de documento: Article