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Defective monocyte plasticity and altered cAMP pathway characterize USB1-mutated poikiloderma with neutropenia Clericuzio type.
Parajuli, Prahlad; Craig, Douglas B; Gadgeel, Manisha; Bagla, Shruti; Wright, Robert E; Chu, Roland; Shanti, Christina M; Thirunagari, Rajeev; Grover, Sudershan K; Ravindranath, Yaddanapudi.
Afiliação
  • Parajuli P; Department of Pharmaceutical and Health Sciences, Eugene Applebaum College of Pharmacy, Wayne State University, Detroit, Michigan, USA.
  • Craig DB; Barbara Ann Karmanos Cancer Institute, Michigan, Detroit, USA.
  • Gadgeel M; Barbara Ann Karmanos Cancer Institute, Michigan, Detroit, USA.
  • Bagla S; Department of Pediatrics, Wayne State University School of Medicine, Detroit, Michigan, USA.
  • Wright RE; Children's Hospital of Michigan, Detroit Medical Center, Detroit, Michigan, USA.
  • Chu R; Central Michigan University, Mt. Pleasant, Michigan, USA.
  • Shanti CM; Department of Pediatrics, Wayne State University School of Medicine, Detroit, Michigan, USA.
  • Thirunagari R; Department of Pharmaceutical and Health Sciences, Eugene Applebaum College of Pharmacy, Wayne State University, Detroit, Michigan, USA.
  • Grover SK; Children's Hospital of Michigan, Detroit Medical Center, Detroit, Michigan, USA.
  • Ravindranath Y; Central Michigan University, Mt. Pleasant, Michigan, USA.
Br J Haematol ; 204(2): 683-693, 2024 02.
Article em En | MEDLINE | ID: mdl-37779259

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Anormalidades da Pele / Neutropenia Limite: Child / Humans / Male Idioma: En Ano de publicação: 2024 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Anormalidades da Pele / Neutropenia Limite: Child / Humans / Male Idioma: En Ano de publicação: 2024 Tipo de documento: Article