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Plummer-Vinson syndrome: a rare occurrence in paediatrics.
Vohra, Wasif Ilyas; Sadiq, Kamran; Iqbal, Mubashir; Rehman, Ayaz-Ur-.
Afiliação
  • Vohra WI; Department of Paediatrics and Child Health, Aga Khan University Hospital, Karachi, Pakistan. dr.wasif17@gmail.com.
  • Sadiq K; Department of Paediatrics and Child Health, Aga Khan University Hospital, Karachi, Pakistan.
  • Iqbal M; Department of Paediatrics and Child Health, Aga Khan University Hospital, Karachi, Pakistan.
  • Rehman AU; Department of Paediatrics and Child Health, Aga Khan University Hospital, Karachi, Pakistan.
BMC Pediatr ; 24(1): 278, 2024 Apr 27.
Article em En | MEDLINE | ID: mdl-38678196
ABSTRACT

BACKGROUND:

Plummer-Vinson syndrome (PVS) is characterized by a triad of symptoms consisting of microcytic hypochromic anaemia, oesophageal webs, and dysphagia. PVS is commonly found in women in the fourth and fifth decades of life and is rarely reported in the paediatric population. CASE PRESENTATION We report the case of a 1-year-old male South Asian child who presented with dysphagia and anaemia for 4 months and frequent episodes of vomiting after ingesting semisolid and solid food. A complete blood analysis revealed microcytic hypochromic anaemia. An oesophagogram revealed circumferential narrowing of the upper thoracic oesophagus. Based on these findings, our suspicion was that the patient had an oesophageal web and vascular ring. Oesophageal dilation was performed with a Savary-Gilliard dilator; initially, 5 mm and 7 mm probes were used, and final dilation with a 9 mm probe was performed.

CONCLUSION:

Although rare in paediatric patients, a high suspicion of this syndrome is necessary in these patients to provide relief to the patient for better growth and development. Iron supplements increase the haemoglobin level but do not subside dysphagia, and oesophageal dilation is needed to open the blocked enteral pathway.
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Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Transtornos de Deglutição / Síndrome de Plummer-Vinson Limite: Humans / Infant / Male Idioma: En Ano de publicação: 2024 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Transtornos de Deglutição / Síndrome de Plummer-Vinson Limite: Humans / Infant / Male Idioma: En Ano de publicação: 2024 Tipo de documento: Article