[Congenital hepatic fibrosis. Study of 26 cases]. / Fibrosis hepática congénita. Estudio de 26 casos.
Acta Gastroenterol Latinoam
; 25(5): 297-303, 1994.
Article
em Es
| MEDLINE
| ID: mdl-7785402
ABSTRACT
We studied 26 children with congenital hepatic fibrosis during the period 1971-1993. About half of the children were about the 6 years old. Only two had brothers with same disease. The chief clinical manifestation was hematemesis associated or not with liver enlargement, predominantly of left lobe. Only one case showed fever and cholangitis. Liver function tests were usually normal. Twenty-two children had portal hypertension. Liver biopsy was of definitive for diagnosis. Seven children died.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Cirrose Hepática
Tipo de estudo:
Diagnostic_studies
Limite:
Child
/
Child, preschool
/
Female
/
Humans
/
Infant
/
Male
Idioma:
Es
Ano de publicação:
1994
Tipo de documento:
Article