Dental and craniofacial findings in a child affected by glycogen storage disease type III.
J Clin Pediatr Dent
; 19(1): 55-60, 1994.
Article
em En
| MEDLINE
| ID: mdl-7865425
ABSTRACT
This paper reports on previously undescribed dentofacial features a child suffering from Glycogen-Storage Disease type III with hepatomegaly and hypertransaminasemia with muscular involvement. Deficient craniofacial development, reduced width of the upper jaw resulting in posterior cross-bite, and taurodontism of the primary dentition were found. Pathogenetic basis for craniofacial abnormalities is discussed. Cooperation between pediatricians and pediatric dentists is strongly recommended for an early diagnosis and treatment of the dentofacial defects of the syndrome.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Crânio
/
Dente Decíduo
/
Doença de Depósito de Glicogênio Tipo III
/
Cavidade Pulpar
Tipo de estudo:
Diagnostic_studies
/
Etiology_studies
/
Screening_studies
Limite:
Child, preschool
/
Female
/
Humans
Idioma:
En
Ano de publicação:
1994
Tipo de documento:
Article