Dyskeratosis congenita associated with Hodgkin's disease.
Eur J Dermatol
; 8(6): 385-7, 1998 Sep.
Article
em En
| MEDLINE
| ID: mdl-9729062
ABSTRACT
Dyskeratosis congenita is a rare, hereditary, multisystem disorder characterized by mucocutaneous changes, pancytopenia and increased incidence of malignancy. Different types of neoplasia have been reported in association with dyskeratosis congenita. We present a second case associated with Hodgkin's disease. Delayed appearance of dermatological signs and association with chronic hepatitis B are other unusual features of this case.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Doença de Hodgkin
/
Hepatite B Crônica
/
Disceratose Congênita
Tipo de estudo:
Diagnostic_studies
/
Observational_studies
/
Prognostic_studies
/
Risk_factors_studies
Limite:
Adult
/
Humans
/
Male
Idioma:
En
Ano de publicação:
1998
Tipo de documento:
Article