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Long-term efficacy and safety of α1 proteinase inhibitor treatment for emphysema caused by severe α1 antitrypsin deficiency: an open-label extension trial (RAPID-OLE).
McElvaney, Noel G; Burdon, Jonathan; Holmes, Mark; Glanville, Allan; Wark, Peter A B; Thompson, Philip J; Hernandez, Paul; Chlumsky, Jan; Teschler, Helmut; Ficker, Joachim H; Seersholm, Niels; Altraja, Alan; Mäkitaro, Riitta; Chorostowska-Wynimko, Joanna; Sanak, Marek; Stoicescu, Paul I; Piitulainen, Eeva; Vit, Oliver; Wencker, Marion; Tortorici, Michael A; Fries, Michael; Edelman, Jonathan M; Chapman, Kenneth R.
Afiliação
  • McElvaney NG; Beaumont Hospital, Royal College of Surgeons in Ireland, Dublin, Ireland. Electronic address: gmcelvaney@rcsi.ie.
  • Burdon J; St Vincent's Hospital, Department of Respiratory Medicine, Fitzroy, VIC, Australia.
  • Holmes M; University of Adelaide and Royal Adelaide Hospital, Department of Thoracic Medicine, Respiratory Clinical Trials Unit, Adelaide, SA, Australia.
  • Glanville A; St Vincent's Hospital, Department of Lung Transplantation and Thoracic Medicine, Darlinghurst, NSW, Australia.
  • Wark PA; Hunter Medical Research Institute, Centre for Asthma and Respiratory Disease, New Lambton, NSW, Australia.
  • Thompson PJ; Institute of Respiratory Medicine & School of Medicine and Pharmacology, University of Western Australia, Crawley, WA, Australia.
  • Hernandez P; Dalhousie University, Division of Respirology, Halifax, NS, Canada.
  • Chlumsky J; Thomayer Hospital, First Medical Faculty, Charles University, Department of Pulmonary Diseases, Prague, Czech Republic.
  • Teschler H; Ruhrlandklinik, Department of Pneumology, West German Lung Center, University Hospital Essen, University Duisburg-Essen, Essen, Germany.
  • Ficker JH; Department of Respiratory Medicine, Allergology and Sleep Medicine, General Hospital Nuernberg, Nuremberg, Germany.
  • Seersholm N; Gentofte Hospital, Pulmonary Department Y, Hellerup, Denmark.
  • Altraja A; University of Tartu, Department of Pulmonary Medicine, Tartu, Estonia.
  • Mäkitaro R; Oulu University Hospital, Department of Internal Medicines, Oulu, Finland.
  • Chorostowska-Wynimko J; National Institute of Tuberculosis and Lung Diseases, Department of Genetics and Clinical Immunology, Warsaw, Poland.
  • Sanak M; Jagiellonian University Medical College, Division of Molecular Biology and Clinical Genetics, Krakow, Poland.
  • Stoicescu PI; Sanador S A Clinical, Central Medical Clinica II, Bucharest, Romania.
  • Piitulainen E; Skane University Hospital, Department of Respiratory Medicine, Lund University, Malmö, Sweden.
  • Vit O; CSL Behring, Bern, Switzerland.
  • Wencker M; conresp, Mainz, Germany.
  • Tortorici MA; CSL Behring, King Of Prussia, PA, USA.
  • Fries M; CSL Behring, King Of Prussia, PA, USA.
  • Edelman JM; CSL Behring, King Of Prussia, PA, USA.
  • Chapman KR; Asthma & Airway Centre, University Health Network and University of Toronto, Toronto, Canada.
Lancet Respir Med ; 5(1): 51-60, 2017 01.
Article em En | MEDLINE | ID: mdl-27916480

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Enfisema Pulmonar / Inibidores de Serina Proteinase / Alfa 1-Antitripsina / Deficiência de alfa 1-Antitripsina Tipo de estudo: Clinical_trials / Diagnostic_studies / Prognostic_studies Limite: Adolescent / Adult / Female / Humans / Male Idioma: En Revista: Lancet Respir Med Ano de publicação: 2017 Tipo de documento: Article País de publicação: Reino Unido

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Enfisema Pulmonar / Inibidores de Serina Proteinase / Alfa 1-Antitripsina / Deficiência de alfa 1-Antitripsina Tipo de estudo: Clinical_trials / Diagnostic_studies / Prognostic_studies Limite: Adolescent / Adult / Female / Humans / Male Idioma: En Revista: Lancet Respir Med Ano de publicação: 2017 Tipo de documento: Article País de publicação: Reino Unido