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Three human aminoacyl-tRNA synthetases have distinct sub-mitochondrial localizations that are unaffected by disease-associated mutations.
González-Serrano, Ligia Elena; Karim, Loukmane; Pierre, Florian; Schwenzer, Hagen; Rötig, Agnès; Munnich, Arnold; Sissler, Marie.
Afiliação
  • González-Serrano LE; From the Université de Strasbourg, CNRS, Architecture et Réactivité de l'ARN, UPR9002, F-67084 Strasbourg, France and.
  • Karim L; From the Université de Strasbourg, CNRS, Architecture et Réactivité de l'ARN, UPR9002, F-67084 Strasbourg, France and.
  • Pierre F; From the Université de Strasbourg, CNRS, Architecture et Réactivité de l'ARN, UPR9002, F-67084 Strasbourg, France and.
  • Schwenzer H; From the Université de Strasbourg, CNRS, Architecture et Réactivité de l'ARN, UPR9002, F-67084 Strasbourg, France and.
  • Rötig A; the INSERM UMR 1163, Laboratory of Genetics of Mitochondrial Disorders, Paris Descartes-Sorbonne Paris Cité University, Imagine Institute, F-75015 Paris, France.
  • Munnich A; the INSERM UMR 1163, Laboratory of Genetics of Mitochondrial Disorders, Paris Descartes-Sorbonne Paris Cité University, Imagine Institute, F-75015 Paris, France.
  • Sissler M; From the Université de Strasbourg, CNRS, Architecture et Réactivité de l'ARN, UPR9002, F-67084 Strasbourg, France and m.sissler@ibmc-cnrs.unistra.fr.
J Biol Chem ; 293(35): 13604-13615, 2018 08 31.
Article em En | MEDLINE | ID: mdl-30006346

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Arginina-tRNA Ligase / Aspartato-tRNA Ligase / Lisina-tRNA Ligase / Mitocôndrias Tipo de estudo: Risk_factors_studies Limite: Female / Humans Idioma: En Revista: J Biol Chem Ano de publicação: 2018 Tipo de documento: Article País de publicação: Estados Unidos

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Arginina-tRNA Ligase / Aspartato-tRNA Ligase / Lisina-tRNA Ligase / Mitocôndrias Tipo de estudo: Risk_factors_studies Limite: Female / Humans Idioma: En Revista: J Biol Chem Ano de publicação: 2018 Tipo de documento: Article País de publicação: Estados Unidos