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Pyridoxal 5'-phosphate and related metabolites in hypophosphatasia: Effects of enzyme replacement therapy.
Akiyama, Tomoyuki; Kubota, Takuo; Ozono, Keiichi; Michigami, Toshimi; Kobayashi, Daisuke; Takeyari, Shinji; Sugiyama, Yuichiro; Noda, Masahiro; Harada, Daisuke; Namba, Noriyuki; Suzuki, Atsushi; Utoyama, Maiko; Kitanaka, Sachiko; Uematsu, Mitsugu; Mitani, Yusuke; Matsunami, Kunihiro; Takishima, Shigeru; Ogawa, Erika; Kobayashi, Katsuhiro.
Afiliação
  • Akiyama T; Department of Child Neurology, Okayama University Graduate School of Medicine, Dentistry and Pharmaceutical Sciences, Okayama, Japan. Electronic address: takiyama@okayama-u.ac.jp.
  • Kubota T; Department of Pediatrics, Osaka University Graduate School of Medicine, Osaka, Japan.
  • Ozono K; Department of Pediatrics, Osaka University Graduate School of Medicine, Osaka, Japan.
  • Michigami T; Department of Bone and Mineral Research, Osaka Women's and Children's Hospital, Osaka, Japan.
  • Kobayashi D; Department of Food and Chemical Toxicology, School of Pharmaceutical Sciences, Health Sciences University of Hokkaido, Hokkaido, Japan.
  • Takeyari S; Department of Pediatrics, Osaka University Graduate School of Medicine, Osaka, Japan.
  • Sugiyama Y; Department of Pediatrics, Nagoya University Graduate School of Medicine, Aichi, Japan.
  • Noda M; Department of Pediatrics, Showa General Hospital, Tokyo, Japan.
  • Harada D; Department of Pediatrics, Osaka Hospital, Japan Community Healthcare Organization (JCHO), Osaka, Japan.
  • Namba N; Department of Pediatrics, Osaka Hospital, Japan Community Healthcare Organization (JCHO), Osaka, Japan.
  • Suzuki A; Department of Neonatology and Pediatrics, Nagoya City University Graduate School of Medical Sciences, Aichi, Japan.
  • Utoyama M; Department of Pediatrics, Faculty of Medicine, University of Miyazaki, Miyazaki, Japan.
  • Kitanaka S; Department of Pediatrics, Graduate School of Medicine, University of Tokyo, Tokyo, Japan.
  • Uematsu M; Department of Pediatrics, Tohoku University Graduate School of Medicine, Miyagi, Japan.
  • Mitani Y; Department of Pediatrics, Kanazawa University Hospital, Ishikawa, Japan.
  • Matsunami K; Department of Pediatrics, Gifu Prefectural General Medical Center, Gifu, Japan.
  • Takishima S; Department of Pediatrics, Soka Municipal Hospital, Saitama, Japan.
  • Ogawa E; Department of Pediatrics and Child Health, Nihon University School of Medicine, Tokyo, Japan.
  • Kobayashi K; Department of Child Neurology, Okayama University Graduate School of Medicine, Dentistry and Pharmaceutical Sciences, Okayama, Japan.
Mol Genet Metab ; 125(1-2): 174-180, 2018 09.
Article em En | MEDLINE | ID: mdl-30049651

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Fosfato de Piridoxal / Proteínas Recombinantes de Fusão / Imunoglobulina G / Fosfatase Alcalina / Terapia de Reposição de Enzimas / Hipofosfatasia Limite: Adolescent / Adult / Child / Child, preschool / Female / Humans / Infant / Male / Newborn Idioma: En Revista: Mol Genet Metab Assunto da revista: BIOLOGIA MOLECULAR / BIOQUIMICA / METABOLISMO Ano de publicação: 2018 Tipo de documento: Article País de publicação: Estados Unidos

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Fosfato de Piridoxal / Proteínas Recombinantes de Fusão / Imunoglobulina G / Fosfatase Alcalina / Terapia de Reposição de Enzimas / Hipofosfatasia Limite: Adolescent / Adult / Child / Child, preschool / Female / Humans / Infant / Male / Newborn Idioma: En Revista: Mol Genet Metab Assunto da revista: BIOLOGIA MOLECULAR / BIOQUIMICA / METABOLISMO Ano de publicação: 2018 Tipo de documento: Article País de publicação: Estados Unidos