Your browser doesn't support javascript.
loading
FGF21 underlies a hormetic response to metabolic stress in methylmalonic acidemia.
Manoli, Irini; Sysol, Justin R; Epping, Madeline W; Li, Lina; Wang, Cindy; Sloan, Jennifer L; Pass, Alexandra; Gagné, Jack; Ktena, Yiouli P; Li, Lingli; Trivedi, Niraj S; Ouattara, Bazoumana; Zerfas, Patricia M; Hoffmann, Victoria; Abu-Asab, Mones; Tsokos, Maria G; Kleiner, David E; Garone, Caterina; Cusmano-Ozog, Kristina; Enns, Gregory M; Vernon, Hilary J; Andersson, Hans C; Grunewald, Stephanie; Elkahloun, Abdel G; Girard, Christiane L; Schnermann, Jurgen; DiMauro, Salvatore; Andres-Mateos, Eva; Vandenberghe, Luk H; Chandler, Randy J; Venditti, Charles P.
Afiliação
  • Manoli I; Medical Genomics and Metabolic Genetics Branch, National Human Genome Research Institute, NIH, Bethesda, Maryland, USA.
  • Sysol JR; Medical Genomics and Metabolic Genetics Branch, National Human Genome Research Institute, NIH, Bethesda, Maryland, USA.
  • Epping MW; Medical Genomics and Metabolic Genetics Branch, National Human Genome Research Institute, NIH, Bethesda, Maryland, USA.
  • Li L; Medical Genomics and Metabolic Genetics Branch, National Human Genome Research Institute, NIH, Bethesda, Maryland, USA.
  • Wang C; Medical Genomics and Metabolic Genetics Branch, National Human Genome Research Institute, NIH, Bethesda, Maryland, USA.
  • Sloan JL; Medical Genomics and Metabolic Genetics Branch, National Human Genome Research Institute, NIH, Bethesda, Maryland, USA.
  • Pass A; Medical Genomics and Metabolic Genetics Branch, National Human Genome Research Institute, NIH, Bethesda, Maryland, USA.
  • Gagné J; Medical Genomics and Metabolic Genetics Branch, National Human Genome Research Institute, NIH, Bethesda, Maryland, USA.
  • Ktena YP; Medical Genomics and Metabolic Genetics Branch, National Human Genome Research Institute, NIH, Bethesda, Maryland, USA.
  • Li L; Kidney Disease Branch, National Institute of Diabetes and Digestive and Kidney Diseases, NIH, Bethesda, Maryland, USA.
  • Trivedi NS; Genome Technology Branch, National Human Genome Research Institute, NIH, Bethesda, Maryland, USA.
  • Ouattara B; Sherbrooke Research and Development Centre, Agriculture and Agri-Food Canada, Sherbrooke, Quebec, Canada.
  • Zerfas PM; Péléforo Gbon Coulibaly University, Korhogo, Ivory Coast.
  • Hoffmann V; Office of Research Services, NIH, Bethesda, Maryland, USA.
  • Abu-Asab M; Office of Research Services, NIH, Bethesda, Maryland, USA.
  • Tsokos MG; Ultrastructural Pathology Section, Center for Cancer Research, NIH, Bethesda, Maryland, USA.
  • Kleiner DE; Ultrastructural Pathology Section, Center for Cancer Research, NIH, Bethesda, Maryland, USA.
  • Garone C; Laboratory of Pathology, National Cancer Institute, NIH, Bethesda, Maryland, USA.
  • Cusmano-Ozog K; Department of Neurology, Columbia University Medical Center, New York, New York, USA.
  • Enns GM; Division of Medical Genetics, Stanford University, Stanford, California, USA.
  • Vernon HJ; Division of Medical Genetics, Stanford University, Stanford, California, USA.
  • Andersson HC; McKusick-Nathans Institute of Genetic Medicine, Johns Hopkins University, Baltimore, Maryland, USA.
  • Grunewald S; Hayward Genetics Center, Tulane University Medical School, New Orleans, Louisiana, USA.
  • Elkahloun AG; Department of Pediatric Metabolic Medicine, Great Ormond Street Hospital for Children Foundation Trust, Institute of Child Health, UCL, London, United Kingdom.
  • Girard CL; Genome Technology Branch, National Human Genome Research Institute, NIH, Bethesda, Maryland, USA.
  • Schnermann J; Sherbrooke Research and Development Centre, Agriculture and Agri-Food Canada, Sherbrooke, Quebec, Canada.
  • DiMauro S; Kidney Disease Branch, National Institute of Diabetes and Digestive and Kidney Diseases, NIH, Bethesda, Maryland, USA.
  • Andres-Mateos E; Department of Neurology, Columbia University Medical Center, New York, New York, USA.
  • Vandenberghe LH; Grousbeck Gene Therapy Center, Schepens Eye Research Institute and Massachusetts Eye and Ear Infirmary, Boston, Massachusetts, USA.
  • Chandler RJ; Ocular Genomics Institute, Department of Ophthalmology, Harvard Medical School, Boston, Massachusetts, USA.
  • Venditti CP; Grousbeck Gene Therapy Center, Schepens Eye Research Institute and Massachusetts Eye and Ear Infirmary, Boston, Massachusetts, USA.
JCI Insight ; 3(23)2018 12 06.
Article em En | MEDLINE | ID: mdl-30518688

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Estresse Fisiológico / Hormese / Fatores de Crescimento de Fibroblastos / Erros Inatos do Metabolismo dos Aminoácidos / Metilmalonil-CoA Mutase Tipo de estudo: Prognostic_studies Limite: Animals / Female / Humans / Male Idioma: En Revista: JCI Insight Ano de publicação: 2018 Tipo de documento: Article País de afiliação: Estados Unidos País de publicação: Estados Unidos

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Estresse Fisiológico / Hormese / Fatores de Crescimento de Fibroblastos / Erros Inatos do Metabolismo dos Aminoácidos / Metilmalonil-CoA Mutase Tipo de estudo: Prognostic_studies Limite: Animals / Female / Humans / Male Idioma: En Revista: JCI Insight Ano de publicação: 2018 Tipo de documento: Article País de afiliação: Estados Unidos País de publicação: Estados Unidos