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Ultrastructural Evidence of Glycosphingolipid Degradation After Enzyme Replacement Therapy in Patients With Fabry Disease.
Onoue, Kenji; Takemura, Genzou; Nakano, Tomoya; Miyazaki, Nagisa; Tsujimoto, Akiko; Watanabe, Takatomo; Okada, Hideshi; Kanamori, Hiromitsu; Sugiura, Junichi; Kanaoka, Koshiro; Ishihara, Satomi; Horii, Manabu; Akai, Yasuhiro; Sakaguchi, Yasuhiro; Saito, Yoshihiko.
Afiliação
  • Onoue K; Cardiovascular Medicine, Nara Medical University.
  • Takemura G; Department of Internal Medicine, Asahi University School of Dentistry.
  • Nakano T; Cardiovascular Medicine, Nara Medical University.
  • Miyazaki N; Department of Internal Medicine, Asahi University School of Dentistry.
  • Tsujimoto A; Department of Cardiology, Gifu University Graduate School of Medicine.
  • Watanabe T; Department of Cardiology, Gifu University Graduate School of Medicine.
  • Okada H; Department of Emergency and Disaster Medicine, Gifu University Graduate School of Medicine.
  • Kanamori H; Department of Cardiology, Gifu University Graduate School of Medicine.
  • Sugiura J; Cardiovascular Medicine, Nara City Hospital.
  • Kanaoka K; Cardiovascular Medicine, Nara Medical University.
  • Ishihara S; Cardiovascular Medicine, Nara Medical University.
  • Horii M; Cardiovascular Medicine, Nara City Hospital.
  • Akai Y; Department of Community-based Medicine, Nara Medical University.
  • Sakaguchi Y; Cardiovascular Medicine, Nara Medical University.
  • Saito Y; Cardiovascular Medicine, Nara Medical University.
Circ J ; 83(10): 2081, 2019 09 25.
Article em En | MEDLINE | ID: mdl-30930427

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Glicoesfingolipídeos / Doença de Fabry / Alfa-Galactosidase / Miócitos Cardíacos / Terapia de Reposição de Enzimas Limite: Aged / Female / Humans / Male / Middle aged Idioma: En Revista: Circ J Assunto da revista: ANGIOLOGIA / CARDIOLOGIA Ano de publicação: 2019 Tipo de documento: Article País de publicação: Japão

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Glicoesfingolipídeos / Doença de Fabry / Alfa-Galactosidase / Miócitos Cardíacos / Terapia de Reposição de Enzimas Limite: Aged / Female / Humans / Male / Middle aged Idioma: En Revista: Circ J Assunto da revista: ANGIOLOGIA / CARDIOLOGIA Ano de publicação: 2019 Tipo de documento: Article País de publicação: Japão