Detalhe da pesquisa
1.
Cystic fibrosis in Europe: improved lung function and longevity - reasons for cautious optimism, but challenges remain.
Eur Respir J
; 63(3)2024 Mar.
Artigo
em Inglês
| MEDLINE | ID: mdl-38302155
2.
Acute respiratory failure due to pulmonary exacerbation in children with cystic fibrosis admitted in a pediatric intensive care unit: outcomes and factors associated with mortality.
Respir Res
; 25(1): 190, 2024 Apr 29.
Artigo
em Inglês
| MEDLINE | ID: mdl-38685088
3.
The French Compassionate Program of elexacaftor-tezacaftor-ivacaftor in people with cystic fibrosis with advanced lung disease and no F508del CFTR variant.
Eur Respir J
; 2023 Feb 16.
Artigo
em Inglês
| MEDLINE | ID: mdl-36796836
4.
Theratyping cystic fibrosis patients to guide elexacaftor/tezacaftor/ivacaftor out-of-label prescription.
Eur Respir J
; 62(4)2023 10.
Artigo
em Inglês
| MEDLINE | ID: mdl-37696564
5.
Volatile metabolites differentiate air-liquid interface cultures after infection with Staphylococcus aureus.
Analyst
; 148(3): 618-627, 2023 Jan 31.
Artigo
em Inglês
| MEDLINE | ID: mdl-36597770
6.
Pharmacological chaperone-rescued cystic fibrosis CFTR-F508del mutant overcomes PRAF2-gated access to endoplasmic reticulum exit sites.
Cell Mol Life Sci
; 79(10): 530, 2022 Sep 27.
Artigo
em Inglês
| MEDLINE | ID: mdl-36167862
7.
Keratin 8 is a scaffolding and regulatory protein of ERAD complexes.
Cell Mol Life Sci
; 79(9): 503, 2022 Sep.
Artigo
em Inglês
| MEDLINE | ID: mdl-36045259
8.
Lung-Adapted Staphylococcus aureus Isolates With Dysfunctional Agr System Trigger a Proinflammatory Response.
J Infect Dis
; 226(7): 1276-1285, 2022 09 28.
Artigo
em Inglês
| MEDLINE | ID: mdl-35524969
9.
Correlating genotype with phenotype using CFTR-mediated whole-cell Cl- currents in human nasal epithelial cells.
J Physiol
; 600(6): 1515-1531, 2022 03.
Artigo
em Inglês
| MEDLINE | ID: mdl-34761808
10.
Saliva for molecular detection of SARS-CoV-2 in pre-school and school-age children.
Environ Microbiol
; 24(10): 4725-4737, 2022 10.
Artigo
em Inglês
| MEDLINE | ID: mdl-36065993
11.
Emerging medicines to improve the basic defect in cystic fibrosis.
Expert Opin Emerg Drugs
; 27(3): 229-239, 2022 09.
Artigo
em Inglês
| MEDLINE | ID: mdl-35731915
12.
Pharmacological chaperones improve intra-domain stability and inter-domain assembly via distinct binding sites to rescue misfolded CFTR.
Cell Mol Life Sci
; 78(23): 7813-7829, 2021 Dec.
Artigo
em Inglês
| MEDLINE | ID: mdl-34714360
13.
Acting on the CFTR Membrane-Spanning Domains Interface Rescues Some Misfolded Mutants.
Int J Mol Sci
; 23(24)2022 Dec 19.
Artigo
em Inglês
| MEDLINE | ID: mdl-36555865
14.
Differential CFTR-Interactome Proximity Labeling Procedures Identify Enrichment in Multiple SLC Transporters.
Int J Mol Sci
; 23(16)2022 Aug 11.
Artigo
em Inglês
| MEDLINE | ID: mdl-36012204
15.
Arterial abnormalities identified in kidneys transplanted into children during the COVID-19 pandemic.
Am J Transplant
; 21(5): 1937-1943, 2021 05.
Artigo
em Inglês
| MEDLINE | ID: mdl-33346946
16.
Involvement of CFTR in the pathogenesis of pulmonary arterial hypertension.
Eur Respir J
; 58(5)2021 11.
Artigo
em Inglês
| MEDLINE | ID: mdl-33926975
17.
Therapeutic pipeline for individuals with cystic fibrosis with mutations nonresponsive to current cystic fibrosis transmembrane conductance regulator modulators.
Curr Opin Pulm Med
; 27(6): 567-574, 2021 11 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-34494979
18.
Real-Life Safety and Effectiveness of Lumacaftor-Ivacaftor in Patients with Cystic Fibrosis.
Am J Respir Crit Care Med
; 201(2): 188-197, 2020 01 15.
Artigo
em Inglês
| MEDLINE | ID: mdl-31601120
19.
Prior infection by seasonal coronaviruses, as assessed by serology, does not prevent SARS-CoV-2 infection and disease in children, France, April to June 2020.
Euro Surveill
; 26(13)2021 04.
Artigo
em Inglês
| MEDLINE | ID: mdl-33797390
20.
Airway Surface Liquid pH Regulation in Airway Epithelium Current Understandings and Gaps in Knowledge.
Int J Mol Sci
; 22(7)2021 Mar 25.
Artigo
em Inglês
| MEDLINE | ID: mdl-33806154