ABSTRACT
Abstract: Fox-Fordyce disease is a relatively infrequent pathology of the apocrine glands that affects almost exclusively young women. The disease is characterized by the presence of pruritic follicular papules mainly in the armpits that respond poorly to treatment and severely affect the patient's quality of life. We report two cases with clinical diagnosis and histopathological confirmation, presenting perifollicular xanthomatosis on histological examination, recently described as a distinctive, consistent, and specific feature of this disease.
Subject(s)
Humans , Female , Adult , Young Adult , Xanthomatosis/pathology , Fox-Fordyce Disease/pathology , Immunohistochemistry , Xanthomatosis/etiology , Fox-Fordyce Disease/complicationsSubject(s)
Humans , Female , Adult , Fox-Fordyce Disease/pathology , Axilla/pathology , Vulva/pathology , Biopsy , Hair Follicle/pathology , Dermis/pathologyABSTRACT
Los angioqueratomas son lesiones vasculares relativamente infrecuentes que consisten en pápulas hiperqueratósicas rojo-violáceas. Éstas pueden ser únicas o múltiples, estar localizadas en un solo segmento corporal o ser generalizadas y estar o no asociadas a otras enfermedades subyacentes. El presente trabajo abordará en profundidad los angioqueratomas localizados y se complementará con una segunda parte en la que se tratarán los angioqueratomas generalizados.
Angiokeratomas are a relatively non-frequent group of vascular lesions that consist on hyperkeratotic red-violaceous papules. Lesions can be solitary or multiple, localized or generalized and may be associated or not with a systemic disease. The present work is a throughout review on localized angiokeratomas and will be complemented with a second part in which generalized angiokeratomas will be discussed.
Subject(s)
Humans , Angiokeratoma , Fox-Fordyce Disease , Porokeratosis , Hyperkeratosis, Epidermolytic , Skin Neoplasms , Tongue DiseasesABSTRACT
Neste estudo relatamos o caso de uma paciente feminina de 12 anos de idade, com lesöes papulosas, pruriginosas, predominantes na regiäo das axilas. As lesöes eram típicas de doença de Fox-Fordyce e o exame anatomopatológico compatível com a hipótese clínica. A conduta terapêutica é abordada, observando-se remissäo das lesöes com o uso tópico de soluçäo de clindamicina em propilenoglicol.
Subject(s)
Humans , Female , Child , Clindamycin/therapeutic use , Fox-Fordyce Disease/diagnosis , Fox-Fordyce Disease/drug therapy , Propylene Glycol/therapeutic useABSTRACT
La patología blanca de la mucosa oral comprende una constelación de enfermedades cuyos cuadros clínicos se asemejan mucho entre sí y se caracterizan por la presentación de una lesión de aspecto blanquesino en la cavidad bucal. Con el fin de remarcar las diferencias entre cada afección, sus diversas evoluciones y pronósticos y alertar sobre aquellas con tendencia cancerígena y pronóstico más ominoso es que se realiza este trabajo. Es también nuestro interés señalar que no debemos olvidar a la cavidad bucal en el examen dermatológico de rutina
Subject(s)
Humans , Candidiasis, Oral/diagnosis , Dyskeratosis Congenita/diagnosis , Fox-Fordyce Disease/diagnosis , Glossitis, Benign Migratory/diagnosis , Leukoplakia, Hairy/diagnosis , Mouth Mucosa/pathology , Nevus/diagnosis , Syphilis/diagnosis , Candidiasis, Oral/pathology , Condylomata Acuminata/diagnosis , Condylomata Acuminata/pathology , Diagnosis, Differential , Focal Epithelial Hyperplasia/diagnosis , Focal Epithelial Hyperplasia/pathology , Fox-Fordyce Disease/pathology , Glossitis, Benign Migratory/pathology , Leukoedema, Oral/diagnosis , Leukoedema, Oral/pathology , Leukoplakia, Hairy/pathology , Leukoplakia, Oral/diagnosis , Leukoplakia, Oral/pathology , Lupus Erythematosus, Systemic/diagnosis , Lupus Erythematosus, Systemic/pathology , Mouth Diseases , Mouth Neoplasms/diagnosis , Mouth Neoplasms/pathology , Papilloma/diagnosis , Papilloma/pathology , Psoriasis/diagnosis , Psoriasis/pathology , Measles/diagnosis , Measles/pathology , Syphilis/pathology , Stomatitis/diagnosis , Stomatitis/etiologySubject(s)
Color , Mouth Diseases , Mouth Mucosa , Aneurysm , Burns , Canavan Disease , Cheilitis , Diagnosis, Differential , Vascular Diseases/congenital , Drug Eruptions , Fox-Fordyce Disease , Glossitis, Benign Migratory , Hemangioma , Leukoedema, Oral , Leukoplakia, Oral , Lichen Planus, Oral , Melanocytes , Melanoma , Pigmentation Disorders , Pinta , Sarcoma, Kaposi , Skin Pigmentation , Stomatitis , Substance-Related Disorders , Tattooing , Nicotiana/adverse effects , Tongue, Hairy , Varicose UlcerABSTRACT
Fox-Fordyce disease is a chronic pruritic papular eiruption, usually appearing in women and presenting a strict localization to the areas bearing apocrine sweat glands. More than 90g, of the cases were seen in women, the majority being in the age group of 13 to 35 years. The present report deals with unusual case of 14-year-old boy who developed Fox-Fordyce disease 6 years ago. To our knowledge, it is extremely rare case in Korea.
Subject(s)
Adolescent , Female , Humans , Male , Fox-Fordyce Disease , Korea , Sweat GlandsABSTRACT
Los autores presentan un caso de enfermedad de Fox-Fordyce, proceso cuyo diagnostico no reviste dificultades cuando se lo tiene presente, por lo tipico de sus manifestaciones.Lo consideran de interes por la poca bibliografia que encuentran sobre el mismo. Hacen una suscinta descripcion de su historia como proceso bien determinado, de su etiopatogenia, histopatologia curso, pronostico y tratamiento, asi como de los diagnosticos que pueden plantearse
Subject(s)
Fox-Fordyce DiseaseABSTRACT
Os autores apresentam um caso, cujo diagnóstico feito pelo exame histopalógico, em paciente do sexo feminino, adulto, de cor branca, queixa antiga de prurido intenso nas regiões axilares, que se fistulizaram posteriormente. Para esclarecimento foi retirada grande extensão da lesão da axila esquerda. O quadro histopatológico mostrou lesões da caracteristica da doença Fox-Fordyce, constituidas por hiprqueratose, tamponamento dos ductos excretores das glândulas, acantose, dilatação dos ductos e dos corpos das glândulas apócrinas, e infiltrado inflamátorio crônico perianexial. O estudo histoquímico foi feito com PAS e AZul de Alcian, constatando positivas as reações para mucopoácidos(Alcian-blue), no material contido nos ductos e glândulas dilatadas. O teste de saliva para glicogênio não alterou os resultados histoquimicos (AU).