ABSTRACT
Biopercular syndrome is a labio-facio-pharyngeal-laryngeal-gloso-masticatory diplegia, with automatic dissociation of movements. Ischemia is the most common etiology when it occurs bilaterally in the opercular area, but it has been also described in patients with bilateral subcortical lesions. There arefew cases described with unilateral lesions. We report a 76-year-old woman who developed a biopercular syndrome caused by unilateral ischemic lesion ofthe right middle cerebral artery confirmed by magnetic resonance imaging and cerebral SPECT.
Subject(s)
Aged , Female , Humans , Deglutition Disorders/etiology , Infarction, Middle Cerebral Artery/complications , Pseudobulbar Palsy/etiology , Voice Disorders/etiology , Deglutition Disorders/therapy , Infarction, Middle Cerebral Artery/diagnosis , Magnetic Resonance Imaging , Pseudobulbar Palsy/therapy , Syndrome , Tomography, X-Ray Computed , Voice Disorders/therapyABSTRACT
Antiphospholipid antibody syndrome (APS) is now recognized as an important risk factor for young stroke. Recurrent stroke seems to be common in patients with APS and a first stroke, recurrent stroke and vascular dementia are feared consequences of APS. We are reporting a case of primary APS with recurrent stroke presenting as pseudobulbar palsy in an young man.
Subject(s)
Adult , Antiphospholipid Syndrome/complications , Brain/diagnostic imaging , Dementia, Vascular/etiology , Humans , Male , Pseudobulbar Palsy/etiology , Recurrence , Stroke/etiology , Tomography, X-Ray ComputedABSTRACT
Os sinais neurológicos na doença de Alzheimer (DA) nä têm sido considerados com o mesmo interesse que as manifestaçöes cognitivas, os de comportamento e psicológicas e os funcionais. A presente revisäo contempla as principais manifestaçöes neurológicas passíveis de ocorrer no curso da DA, divididas em quatro tópicos: sinais extrapiramidas e discinesias (parkinsonismo, discinesia oromandibular, mioclonia), sinais piramidais, paralisia pseudobulbar), disfunçäo integradativa (distúrbios de postura, transtornos de marcha, sinais cerebelares, paraplegia em flexäo de origem cerebral) crises convulsivas. Baseados em ampla revisäo bibliográfica, säo apresentados dados numéricos representativos da pervalência dos sinais neurológicos mais importantes de manifestaçäo no curso da doença e comparados com sua presença em condiçöes normais. Säo ainda feitas consideraçöes de correlaçäo dos sinais neurológicos a diversas características evolutivas e da sua importância em relaçäo ao prognóstico da doença