An autopsy series of an oft-missed ante-mortem diagnosis: hemophagocytic lymphohistiocytosis
Autops. Case Rep
; 11: e2021243, 2021. tab, graf
Article
in En
| LILACS
| ID: biblio-1285402
Responsible library:
BR26.7
ABSTRACT
Hemophagocytic lymphohistiocytosis (HLH) is a rare and potentially fatal syndrome resulting from a hyperactivated immune system. Diverse patient profiles and clinical presentations often result in misdiagnosis. This article describes the varied clinical presentations and autopsy findings in three patients with this entity. The etiopathogenesis of HLH, its disparate and confounding clinical features, the diagnostic criteria, and management principles are also briefly reviewed.
Key words
Full text:
1
Index:
LILACS
Main subject:
Lymphohistiocytosis, Hemophagocytic
Type of study:
Diagnostic_studies
Limits:
Adult
/
Humans
/
Male
Language:
En
Journal:
Autops. Case Rep
Journal subject:
Anatomia
/
Patologia Cl¡nica
/
Patologia Legal
Year:
2021
Type:
Article