Encefalitis autoinmunitaria asociada a anticuerpos contra el receptor N-metil-D-aspartato: presentación de dos casos / Autoimmune encephalitis associated to antibodies against the N-methyl-D-aspartate receptor: Report of two cases
Biomédica (Bogotá)
; 37(supl.1): 20-25, abr. 2017. tab, graf
Article
in Es
| LILACS
| ID: biblio-888506
Responsible library:
BR1.1
RESUMEN
Resumen La encefalitis asociada a anticuerpos contra receptores N-metil-D-aspartato es un síndrome neurológico que se presenta más comúnmente en mujeres jóvenes y frecuentemente se asocia al teratoma de ovario. Se caracteriza por un cuadro clínico agudo con síntomas generales inespecíficos que evoluciona hacia deterioro neurológico, psicosis y convulsiones; en su etapa más avanzada, se asocia con movimientos anormales y disautonomía. Se reportan dos casos en mujeres de 23 y 12 años. Dada su baja incidencia, se explica el proceso clínico que llevó a su diagnóstico y las opciones de tratamiento empleadas.
ABSTRACT
Abstract Anti-N-methyl-D-aspartate receptor encephalitis is a neurological syndrome that is more common in young women and is often associated with ovarian teratoma. It is characterized by acute general unspecific symptoms that evolve to neurological deterioration, psychosis and seizures. In its more advanced stage it is associated with abnormal movements and dysautonomia. We report two cases in women of 23 and 12 years of age. Given its low incidence, we present the clinical exercise that led to their diagnoses and the treatment options employed.
Key words
Full text:
1
Index:
LILACS
Main subject:
Ovarian Neoplasms
/
Seizures
/
Teratoma
/
Receptors, N-Methyl-D-Aspartate
/
Encephalitis
/
Hashimoto Disease
/
Anti-N-Methyl-D-Aspartate Receptor Encephalitis
Type of study:
Risk_factors_studies
Limits:
Female
/
Humans
Language:
Es
Journal:
Biomédica (Bogotá)
Journal subject:
MEDICINA
Year:
2017
Type:
Article