Manejo de fractura en hueso patológico en la infancia: picnodisostosis / Management of fractures in pathological bone in childhood: pycnodysostosis
Rev. chil. ortop. traumatol
; 57(2): 54-59, mayo-ago. 2016. ilus, tab
Article
in Es
| LILACS
| ID: biblio-909709
Responsible library:
CL1.1
RESUMEN
La picnodisostosis es una enfermedad poco común que pertenece a las displasias esqueléticas que presentan fragilidad ósea y fracturas frecuentes. Radiológicamente se caracteriza por incremento de la densidad y fragilidad óseas. OBJETIVO:
Presentar el caso de un escolar con displasia esquelética con fracturas en hueso patológico y manejo quirúrgico. CASO CLÍNICO Escolar de sexo femenino, con antecedente de picnodisostosis detectado en etapa preescolar. Consulta posterior a caída de bicicleta con fractura de ambos fémures que se manejan quirúrgicamente con placa de compresión bloqueada.ABSTRACT
Pycnodysostosis is a rare condition within skeletal dysplasias presenting with brittle bones and frequent fractures. Radiologically, it is characterised by increased bone density and fragility. OBJECTIVE:
To present the case of a primary schoolchild with skeletal dysplasia with pathological bone fractures and their surgical management. CASE REPORT A female primary schoolchild with a history of pycnodysostosis detected during the pre-school period. She was seen after bicycle fall that resulted in the fracture of both femurs, that were surgically managed with a locking compression plate.Key words
Full text:
1
Index:
LILACS
Main subject:
Femoral Fractures
/
Pycnodysostosis
/
Fracture Fixation, Internal
Type of study:
Diagnostic_studies
Limits:
Child
/
Female
/
Humans
Language:
Es
Journal:
Rev. chil. ortop. traumatol
Journal subject:
ORTOPEDIA
/
TRAUMATOLOGIA
Year:
2016
Type:
Article